Short stature-advanced bone age-early-onset osteoarthritis syndrome

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ORPHA:435804OMIM:165800M89.8
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8Treatment centers

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Overview

Short stature-advanced bone age-early-onset osteoarthritis syndrome is an extremely rare genetic condition that affects how bones and joints develop and age. People with this syndrome are shorter than expected for their age and sex, but their bones mature faster than normal, which is called advanced bone age. This means that on X-rays, the bones look like those of someone older. In addition, people with this condition develop osteoarthritis — the wearing down of cartilage in the joints — much earlier than usual, often starting in childhood or young adulthood rather than later in life as is typical. The main symptoms include short stature, joint pain and stiffness from early-onset osteoarthritis, and skeletal abnormalities that can be seen on imaging. The joints most commonly affected may include the hips, knees, and hands. Over time, the osteoarthritis can become progressively worse, leading to reduced mobility and chronic pain. Because this syndrome is so rare, there is no specific cure or targeted therapy available. Treatment focuses on managing symptoms, particularly pain control and maintaining joint function. Physical therapy, pain medications, and in some cases joint replacement surgery may be needed. Ongoing research into the genetic causes of this condition may eventually lead to more targeted treatments.

Key symptoms:

Short stature or being shorter than expectedBones that mature faster than normal (advanced bone age)Early-onset joint pain and stiffness (osteoarthritis)Reduced range of motion in jointsJoint swellingChronic pain in hips, knees, or handsDifficulty walking or moving due to joint problemsSkeletal abnormalities visible on X-raysProgressive joint damage over timeLimb length differences or disproportionate body segments

Clinical phenotype terms (5)— hover any for plain English
Developmental stagnationHP:0007281
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Short stature-advanced bone age-early-onset osteoarthritis syndrome.

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No actively recruiting trials found for Short stature-advanced bone age-early-onset osteoarthritis syndrome at this time.

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No specialists are currently listed for Short stature-advanced bone age-early-onset osteoarthritis syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Short stature-advanced bone age-early-onset osteoarthritis syndrome.

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Community

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Latest news about Short stature-advanced bone age-early-onset osteoarthritis syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the specific genetic cause of my child's condition, and should we pursue further genetic testing?,How quickly is the osteoarthritis likely to progress, and what can we do to slow it down?,What types of physical activity are safe and beneficial for my child's joints?,Are there any clinical trials or new treatments being studied for this condition?,Should we consider growth hormone evaluation or treatment?,What signs should prompt us to seek urgent medical attention?,How often should we schedule follow-up imaging and specialist visits?

Common questions about Short stature-advanced bone age-early-onset osteoarthritis syndrome

What is Short stature-advanced bone age-early-onset osteoarthritis syndrome?

Short stature-advanced bone age-early-onset osteoarthritis syndrome is an extremely rare genetic condition that affects how bones and joints develop and age. People with this syndrome are shorter than expected for their age and sex, but their bones mature faster than normal, which is called advanced bone age. This means that on X-rays, the bones look like those of someone older. In addition, people with this condition develop osteoarthritis — the wearing down of cartilage in the joints — much earlier than usual, often starting in childhood or young adulthood rather than later in life as is typ

How is Short stature-advanced bone age-early-onset osteoarthritis syndrome inherited?

Short stature-advanced bone age-early-onset osteoarthritis syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Short stature-advanced bone age-early-onset osteoarthritis syndrome typically begin?

Typical onset of Short stature-advanced bone age-early-onset osteoarthritis syndrome is childhood. Age of onset can vary across affected individuals.