Scott syndrome

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ORPHA:806OMIM:262890D69.8
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17Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Scott syndrome is an extremely rare inherited bleeding disorder that affects how your blood clots. In a healthy person, when you get a cut or injury, small blood cells called platelets become activated and expose a substance called phosphatidylserine on their surface. This substance is essential for triggering the clotting process. In Scott syndrome, platelets and certain other blood cells cannot properly move phosphatidylserine to their outer surface, which means the blood clotting process does not work as it should. This leads to a tendency to bleed more than normal, especially after injuries, surgeries, or dental procedures. Women with Scott syndrome may experience particularly heavy menstrual periods. The condition was first described in a patient named Ms. Scott in the 1970s, which is how it got its name. It is also sometimes called Scott platelet disorder. Symptoms can range from mild to moderate bleeding problems. Some people may not realize they have the condition until they face a situation that challenges their clotting system, such as surgery or trauma. Because it is so rare, Scott syndrome is often underdiagnosed or misdiagnosed as another bleeding disorder. There is currently no cure for Scott syndrome. Treatment focuses on managing and preventing bleeding episodes. Fresh frozen plasma, platelet transfusions, and medications that help stabilize clots may be used when needed. Careful planning before any surgical or dental procedure is essential to reduce the risk of excessive bleeding.

Key symptoms:

Excessive bleeding after surgery or dental proceduresHeavy menstrual periods in womenEasy bruisingProlonged bleeding from cuts or woundsNosebleeds that are hard to stopBleeding after childbirthBleeding into muscles or joints in severe casesDelayed wound healing

Clinical phenotype terms (7)— hover any for plain English
Prolonged bleeding after surgeryHP:0004846Post-partum hemorrhageHP:0011891
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Scott syndrome.

View clinical trials →

No actively recruiting trials found for Scott syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Scott syndrome community →

Specialists

17 foundView all specialists →
GL
Gillian C Lowe
EDGEWATER, MD
Specialist
2 Scott syndrome publications
SR
Solène Remizé
Specialist
1 Scott syndrome publication
SA
Stéphanie Arpin
Specialist
1 Scott syndrome publication
NM
Neil V Morgan
FLORENCE, SC
Specialist
2 Scott syndrome publications
SM
Samantha J Montague
LUPTON, MI
Specialist
2 Scott syndrome publications
NP
Natasha J Pavey
Specialist
2 Scott syndrome publications
PB
Patricia Bignell
Specialist
2 Scott syndrome publications
CF
Carl Fratter
Specialist
2 Scott syndrome publications
NP
Natalie S Poulter
Specialist
2 Scott syndrome publications
BL
Bas De Laat
Specialist
2 Scott syndrome publications
DH
Dana Huskens
Specialist
2 Scott syndrome publications
ST
Steven G Thomas
Specialist
2 Scott syndrome publications
MJ
Médéric Jeanne
Specialist
1 Scott syndrome publication
NR
Nathalie Ronce
Specialist
1 Scott syndrome publication
GB
Geneviève Baujat
Specialist
1 Scott syndrome publication
AD
Amin A Mohammad, Ph. D
Specialist
PI on 1 active trial
LG
Lélia GRUNEBAUM
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Scott syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Scott syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What precautions should I take before any surgery or dental procedure?,Should I carry emergency medication with me, and if so, what kind?,Are there any activities or sports I should avoid?,How should heavy menstrual bleeding be managed in my case?,Should my family members be tested for Scott syndrome?,What should I do if I experience uncontrolled bleeding at home?,Are there any new treatments or clinical trials I should know about?

Common questions about Scott syndrome

What is Scott syndrome?

Scott syndrome is an extremely rare inherited bleeding disorder that affects how your blood clots. In a healthy person, when you get a cut or injury, small blood cells called platelets become activated and expose a substance called phosphatidylserine on their surface. This substance is essential for triggering the clotting process. In Scott syndrome, platelets and certain other blood cells cannot properly move phosphatidylserine to their outer surface, which means the blood clotting process does not work as it should. This leads to a tendency to bleed more than normal, especially after injurie

How is Scott syndrome inherited?

Scott syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Scott syndrome?

17 specialists and care centers treating Scott syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.