Roch-Leri mesosomatous lipomatosis

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Overview

Roch-Leri mesosomatous lipomatosis, also known as Roch-Leri syndrome or mesosomatous lipomatosis, is a very rare condition where multiple fatty lumps called lipomas grow on the body, particularly on the trunk and upper limbs. The word 'mesosomatous' refers to the middle part of the body, which is where these fatty growths tend to cluster. These lipomas are benign, meaning they are not cancerous, but they can grow large enough to cause discomfort, limit movement, or affect appearance in ways that impact daily life and self-confidence. The fatty lumps develop under the skin and can vary in size. In some people, they remain small and cause little trouble. In others, they grow larger and may press on nearby nerves or tissues, causing pain or a feeling of tightness. The condition is classified under lipomatosis disorders, which are conditions involving abnormal fat deposits in the body. Treatment is mainly focused on managing symptoms. Surgical removal of troublesome lipomas is the most common approach when lumps cause pain, restrict movement, or create cosmetic concerns. There is no known cure or medication that stops new lipomas from forming. Because this condition is so rare, research is limited and most care is guided by general lipomatosis management principles.

Key symptoms:

Multiple soft, movable fatty lumps under the skinLumps mainly on the trunk, shoulders, and upper armsDiscomfort or pain if lumps press on nervesFeeling of tightness or heaviness in affected areasChanges in body shape or appearance due to fatty growthsPossible restricted movement if lumps grow near jointsGradual increase in number or size of lumps over time

Clinical phenotype terms (4)— hover any for plain English
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Roch-Leri mesosomatous lipomatosis.

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No actively recruiting trials found for Roch-Leri mesosomatous lipomatosis at this time.

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No specialists are currently listed for Roch-Leri mesosomatous lipomatosis.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Roch-Leri mesosomatous lipomatosis.

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Community

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Caregiver Resources

NORD Caregiver Resources

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Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How certain are you about this diagnosis, and what other conditions were ruled out?,Should I have genetic testing to look for a related hereditary condition?,Which of my lipomas are most likely to need surgical removal, and when?,How often should I come in for monitoring, and what changes should prompt an urgent visit?,Are there any clinical trials or research studies I could participate in?,Could my family members be at risk, and should they be evaluated?,Are there any lifestyle changes or treatments that might slow the growth of new lipomas?

Common questions about Roch-Leri mesosomatous lipomatosis

What is Roch-Leri mesosomatous lipomatosis?

Roch-Leri mesosomatous lipomatosis, also known as Roch-Leri syndrome or mesosomatous lipomatosis, is a very rare condition where multiple fatty lumps called lipomas grow on the body, particularly on the trunk and upper limbs. The word 'mesosomatous' refers to the middle part of the body, which is where these fatty growths tend to cluster. These lipomas are benign, meaning they are not cancerous, but they can grow large enough to cause discomfort, limit movement, or affect appearance in ways that impact daily life and self-confidence. The fatty lumps develop under the skin and can vary in size

At what age does Roch-Leri mesosomatous lipomatosis typically begin?

Typical onset of Roch-Leri mesosomatous lipomatosis is adult. Age of onset can vary across affected individuals.