Rare female infertility due to an anomaly of ovarian function of genetic origin

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:400022
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Rare female infertility due to an anomaly of ovarian function of genetic origin is a group of uncommon conditions in which a woman's ovaries do not work properly because of changes (mutations) in one or more genes. The ovaries are the organs that produce eggs and important hormones like estrogen and progesterone. When the ovaries do not function correctly due to a genetic cause, a woman may have difficulty becoming pregnant or may be completely unable to conceive naturally. This condition can present in different ways depending on the specific gene involved. Some women may experience premature ovarian insufficiency (POI), where the ovaries stop working before age 40. Others may have problems with egg development, ovulation (the release of eggs), or the hormonal signals that control the menstrual cycle. Symptoms often include irregular or absent menstrual periods, difficulty getting pregnant, and sometimes signs of low estrogen such as hot flashes, vaginal dryness, or mood changes. The treatment landscape varies depending on the underlying genetic cause and the severity of ovarian dysfunction. Options may include hormone replacement therapy to manage symptoms of low estrogen, fertility treatments such as in vitro fertilization (IVF) — sometimes using donor eggs — and supportive care for associated health concerns like bone health. Genetic counseling is an important part of care, as some forms can be passed on to future generations. Research is ongoing to better understand the many genes involved and to develop more targeted treatments.

Key symptoms:

Irregular menstrual periodsAbsent menstrual periodsDifficulty getting pregnantHot flashesNight sweatsVaginal drynessLow sex driveMood swings or depressionDifficulty sleepingThinning hairDry skinDecreased bone densityPain during intercourseFatigue

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Rare female infertility due to an anomaly of ovarian function of genetic origin.

View clinical trials →

No actively recruiting trials found for Rare female infertility due to an anomaly of ovarian function of genetic origin at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Rare female infertility due to an anomaly of ovarian function of genetic origin community →

No specialists are currently listed for Rare female infertility due to an anomaly of ovarian function of genetic origin.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Rare female infertility due to an anomaly of ovarian function of genetic origin.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Rare female infertility due to an anomaly of ovarian function of genetic originForum →

No community posts yet. Be the first to share your experience with Rare female infertility due to an anomaly of ovarian function of genetic origin.

Start the conversation →

Latest news about Rare female infertility due to an anomaly of ovarian function of genetic origin

No recent news articles for Rare female infertility due to an anomaly of ovarian function of genetic origin.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic cause has been identified for my ovarian dysfunction, and what does it mean for me?,Is there any chance my ovarian function could improve, or is the decline permanent?,What are my realistic options for having a biological child, and what are the success rates?,Should I consider fertility preservation such as egg freezing, and is it still an option for me?,Do I need hormone replacement therapy, and what are the benefits and risks?,Could my condition affect other family members, and should they be tested?,What long-term health risks should I be aware of, such as bone loss or heart disease?

Common questions about Rare female infertility due to an anomaly of ovarian function of genetic origin

What is Rare female infertility due to an anomaly of ovarian function of genetic origin?

Rare female infertility due to an anomaly of ovarian function of genetic origin is a group of uncommon conditions in which a woman's ovaries do not work properly because of changes (mutations) in one or more genes. The ovaries are the organs that produce eggs and important hormones like estrogen and progesterone. When the ovaries do not function correctly due to a genetic cause, a woman may have difficulty becoming pregnant or may be completely unable to conceive naturally. This condition can present in different ways depending on the specific gene involved. Some women may experience premature

At what age does Rare female infertility due to an anomaly of ovarian function of genetic origin typically begin?

Typical onset of Rare female infertility due to an anomaly of ovarian function of genetic origin is adult. Age of onset can vary across affected individuals.