Rare epithelial tumor of rectum

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ORPHA:423998
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1Specialists8Treatment centers

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Overview

A rare epithelial tumor of the rectum is an uncommon growth that starts in the lining cells (epithelial cells) of the rectum, which is the last section of the large intestine before the anus. These tumors are different from the more common types of rectal cancer and can include unusual subtypes such as rare adenocarcinoma variants, squamous cell carcinomas of the rectum, neuroendocrine tumors, or other uncommon epithelial growths. Because they are rare, they may not behave exactly like typical rectal cancers, and treatment decisions can be more complex. The rectum plays an important role in storing and passing stool. When a tumor grows in this area, it can interfere with normal bowel function and cause a range of symptoms. People may notice changes in their bowel habits, rectal bleeding, or a feeling that the bowel has not fully emptied. Some tumors grow slowly, while others can spread more quickly to nearby lymph nodes or other organs. Treatment usually involves a combination of surgery, radiation therapy, and chemotherapy, depending on the specific tumor type and how far it has spread. Because these tumors are so rare, care at a specialized cancer center with experience in rare gastrointestinal cancers is strongly recommended. Early detection generally leads to better outcomes.

Also known as:

Key symptoms:

Rectal bleeding or blood in the stoolChanges in bowel habits, such as diarrhea or constipationFeeling that the bowel has not fully emptied after a bowel movementNarrow or pencil-thin stoolsPain or discomfort in the lower abdomen or rectumUnexplained weight lossFatigue or tirednessA lump or mass that can be felt in or near the rectumMucus in the stoolAnemia (low red blood cell count) causing weakness or pale skin

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Rare epithelial tumor of rectum.

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No actively recruiting trials found for Rare epithelial tumor of rectum at this time.

New trials open frequently. Follow this disease to get notified.

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Specialists

1 foundView all specialists →
CD
Camila MV Moniz, Doctor
SAN ANTONIO, TX
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Rare epithelial tumor of rectum.

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Community

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Latest news about Rare epithelial tumor of rectum

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What exact type of rare epithelial tumor do I have, and how does that affect my treatment options?,Has my tumor been tested for genetic markers like microsatellite instability or mismatch repair deficiency, and what do the results mean for my treatment?,Should I have genetic testing to find out if a hereditary syndrome may have caused this tumor?,What is the goal of my treatment — to cure the cancer or to control it?,Will I need a colostomy, and if so, is it likely to be temporary or permanent?,Are there any clinical trials I might be eligible for given how rare this tumor type is?,What support services are available to help me and my family cope with this diagnosis?

Common questions about Rare epithelial tumor of rectum

What is Rare epithelial tumor of rectum?

A rare epithelial tumor of the rectum is an uncommon growth that starts in the lining cells (epithelial cells) of the rectum, which is the last section of the large intestine before the anus. These tumors are different from the more common types of rectal cancer and can include unusual subtypes such as rare adenocarcinoma variants, squamous cell carcinomas of the rectum, neuroendocrine tumors, or other uncommon epithelial growths. Because they are rare, they may not behave exactly like typical rectal cancers, and treatment decisions can be more complex. The rectum plays an important role in s

How is Rare epithelial tumor of rectum inherited?

Rare epithelial tumor of rectum follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Rare epithelial tumor of rectum typically begin?

Typical onset of Rare epithelial tumor of rectum is adult. Age of onset can vary across affected individuals.

Which specialists treat Rare epithelial tumor of rectum?

1 specialists and care centers treating Rare epithelial tumor of rectum are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.