Ramos-Arroyo syndrome

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ORPHA:1051OMIM:122430Q87.8
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Overview

Ramos-Arroyo syndrome is a very rare condition that affects multiple parts of the body, most notably the eyes and the nervous system. It was first described by doctors Ramos and Arroyo, and only a small number of cases have been reported in the medical literature. The syndrome is sometimes referred to as a congenital syndrome with coloboma and other eye abnormalities combined with intellectual disability and distinctive physical features. People with Ramos-Arroyo syndrome are typically born with problems affecting the structure of the eyes, including coloboma (a gap or hole in part of the eye), which can lead to vision problems or even blindness. Many individuals also have some degree of intellectual disability, meaning they may need extra support with learning and daily tasks. Other features can include unusual facial features, hearing difficulties, and problems with other organ systems. Because this condition is so rare, there is no specific cure, and treatment focuses on managing each symptom as it appears. A team of specialists — including eye doctors, neurologists, and developmental pediatricians — typically works together to support affected individuals. Early intervention programs, special education, and vision rehabilitation can make a meaningful difference in quality of life.

Also known as:

Key symptoms:

Coloboma (a gap or missing piece in part of the eye)Vision problems or reduced visionIntellectual disability or learning difficultiesDistinctive facial featuresHearing loss or difficulty hearingSmall head size (microcephaly)Short statureDelayed development and milestonesAbnormalities of other internal organs

Clinical phenotype terms (46)— hover any for plain English
Abnormal midface morphologyHP:0000309Decreased corneal sensationHP:0012155Broad faceHP:0000283Nasolacrimal duct obstructionHP:0000579Severe failure to thriveHP:0001525Absent retinal pigment epitheliumHP:0007980Bilateral sensorineural hearing impairmentHP:0008619Concave nasal ridgeHP:0011120
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Ramos-Arroyo syndrome.

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No actively recruiting trials found for Ramos-Arroyo syndrome at this time.

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No specialists are currently listed for Ramos-Arroyo syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Ramos-Arroyo syndrome.

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Community

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Latest news about Ramos-Arroyo syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What tests should we do to confirm the diagnosis and look for a genetic cause?,What specialists should be part of our care team, and how often should we see them?,What early intervention or therapy programs do you recommend starting right away?,Are there any complications we should watch for, and what are the warning signs?,How will this condition affect my child's development and ability to learn?,Are there any clinical trials or research studies we could participate in?,Where can we find support groups or connect with other families affected by this condition?

Common questions about Ramos-Arroyo syndrome

What is Ramos-Arroyo syndrome?

Ramos-Arroyo syndrome is a very rare condition that affects multiple parts of the body, most notably the eyes and the nervous system. It was first described by doctors Ramos and Arroyo, and only a small number of cases have been reported in the medical literature. The syndrome is sometimes referred to as a congenital syndrome with coloboma and other eye abnormalities combined with intellectual disability and distinctive physical features. People with Ramos-Arroyo syndrome are typically born with problems affecting the structure of the eyes, including coloboma (a gap or hole in part of the eye

How is Ramos-Arroyo syndrome inherited?

Ramos-Arroyo syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Ramos-Arroyo syndrome typically begin?

Typical onset of Ramos-Arroyo syndrome is neonatal. Age of onset can vary across affected individuals.