Primary pediatric heart tumor

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ORPHA:875C38.0D15.1
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8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Primary pediatric heart tumors are rare growths that form inside or on the heart in children, including newborns and infants. These tumors can be either benign (not cancerous) or malignant (cancerous), though the majority found in children are benign. The most common type in children is called a cardiac rhabdomyoma, followed by fibromas, myxomas, and teratomas. Malignant tumors, such as sarcomas, are much rarer but more serious. The ICD-10 codes C38.0 (malignant) and D15.1 (benign) reflect this important distinction. These tumors can affect the heart in several ways depending on their size and location. They may block blood flow through the heart, interfere with the heart's electrical system causing abnormal rhythms, or press on surrounding structures. Some tumors cause no symptoms at all and are found by accident during an ultrasound. Others can cause serious problems from birth. Symptoms vary widely but can include an irregular heartbeat, difficulty breathing, poor feeding in infants, bluish skin color, and fainting. Treatment depends on the tumor type. Many benign tumors, especially rhabdomyomas linked to a condition called tuberous sclerosis, may shrink on their own over time. Others require surgery, medication, or in rare cases, more intensive cancer treatment. Early detection and care by a specialized heart team greatly improves outcomes for most children.

Also known as:

Key symptoms:

Irregular or abnormally fast heartbeat (arrhythmia)Difficulty breathing or shortness of breathBluish tint to the skin, lips, or fingernails (cyanosis)Poor feeding or difficulty eating in infantsFatigue or unusual tirednessFainting or loss of consciousnessSwelling in the legs, abdomen, or faceHeart murmur detected by a doctorChest pain or discomfortSeizures (especially if linked to tuberous sclerosis)Slow weight gain or failure to thrive in infantsSudden cardiac arrest in severe cases

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

3 events
Nov 2025Evaluation of Cardiac and Endothelial Function in Children and Adolescents Treated With Anthracycline

Fondazione Policlinico Universitario Agostino Gemelli IRCCS

TrialNOT YET RECRUITING
Nov 2024Cancer Therapy-related Cardiac Dysfunction Occuring in Children Treated by Anticancer Drugs for Malignancies

University Hospital, Caen

TrialNOT YET RECRUITING
Feb 2021Pediatric In-Hospital Cardiac Arrest International Registry (PACHIN)

Jimena del Castillo

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Primary pediatric heart tumor.

View clinical trials →

No actively recruiting trials found for Primary pediatric heart tumor at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Primary pediatric heart tumor community →

No specialists are currently listed for Primary pediatric heart tumor.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Primary pediatric heart tumor.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Primary pediatric heart tumor

Disease timeline:

New recruiting trial: Pediatric In-Hospital Cardiac Arrest International Registry (PACHIN)

A new clinical trial is recruiting patients for Primary pediatric heart tumor

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of heart tumor does my child have, and is it benign or malignant?,Does my child need treatment right away, or is watchful waiting appropriate?,Should my child be tested for tuberous sclerosis or another genetic condition?,What are the signs that the tumor is growing or causing more problems, and when should I call you or go to the emergency room?,Are there any activity restrictions my child needs to follow?,What does long-term follow-up look like, and how often will my child need heart imaging?,Are there any clinical trials or newer treatments we should consider?

Common questions about Primary pediatric heart tumor

What is Primary pediatric heart tumor?

Primary pediatric heart tumors are rare growths that form inside or on the heart in children, including newborns and infants. These tumors can be either benign (not cancerous) or malignant (cancerous), though the majority found in children are benign. The most common type in children is called a cardiac rhabdomyoma, followed by fibromas, myxomas, and teratomas. Malignant tumors, such as sarcomas, are much rarer but more serious. The ICD-10 codes C38.0 (malignant) and D15.1 (benign) reflect this important distinction. These tumors can affect the heart in several ways depending on their size an

At what age does Primary pediatric heart tumor typically begin?

Typical onset of Primary pediatric heart tumor is neonatal. Age of onset can vary across affected individuals.