Polymicrogyria

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:35981
Who is this for?
Show terms as
3Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Polymicrogyria (PMG) is a brain development condition where the surface of the brain forms too many small, unusually shaped folds. Normally, the brain develops smooth, well-organized folds called gyri. In polymicrogyria, these folds are too numerous and too small, and the brain's outer layer (cortex) is not organized the way it should be. This happens before birth, usually between the 16th and 24th week of pregnancy, when the brain is still forming. The name comes from Greek and Latin words meaning 'many small folds.' It may also be called cortical dysplasia or malformation of cortical development in some medical settings. Polymicrogyria can affect one part of the brain (focal) or many areas (diffuse or bilateral). The most common form affects both sides of the brain around the area that controls movement and sensation, called bilateral perisylvian polymicrogyria (BPP). Symptoms vary widely depending on how much of the brain is affected and where. Common problems include epilepsy (seizures), intellectual disability, difficulty speaking or swallowing, muscle weakness or stiffness, and developmental delays. Some people have mild symptoms, while others are more severely affected. There is currently no cure for polymicrogyria. Treatment focuses on managing symptoms, especially seizures, using anti-seizure medications. Speech therapy, physical therapy, occupational therapy, and special education support can greatly improve quality of life. A team of specialists usually works together to help each person reach their full potential.

Key symptoms:

Seizures or epilepsyIntellectual disability or learning difficultiesDelayed speech and language developmentDifficulty swallowing (dysphagia)Muscle weakness or stiffness (spasticity)Problems with coordination and balanceDevelopmental delays (sitting, walking, talking later than expected)Behavioral or psychiatric problemsDifficulty controlling facial musclesVision problems in some casesFeeding difficulties in infancyDrooling

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Polymicrogyria.

View clinical trials →

No actively recruiting trials found for Polymicrogyria at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Polymicrogyria community →

Specialists

3 foundView all specialists →
CP
Christopher A. Walsh, M.D., Ph.D.
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Polymicrogyria.

Search all travel grants →NORD Financial Assistance ↗

Community

Open PolymicrogyriaForum →

No community posts yet. Be the first to share your experience with Polymicrogyria.

Start the conversation →

Latest news about Polymicrogyria

No recent news articles for Polymicrogyria.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What part of my child's brain is affected, and how does that explain their specific symptoms?,Should we do genetic testing, and which type would be most helpful for our family?,What anti-seizure medications do you recommend, and what are the side effects we should watch for?,What therapies (speech, physical, occupational) should we start, and how often?,Is there any chance the seizures could be controlled with surgery or other treatments if medications don't work?,What should I do if my child has a prolonged seizure at home?,Are there any clinical trials or research studies we should know about?

Common questions about Polymicrogyria

What is Polymicrogyria?

Polymicrogyria (PMG) is a brain development condition where the surface of the brain forms too many small, unusually shaped folds. Normally, the brain develops smooth, well-organized folds called gyri. In polymicrogyria, these folds are too numerous and too small, and the brain's outer layer (cortex) is not organized the way it should be. This happens before birth, usually between the 16th and 24th week of pregnancy, when the brain is still forming. The name comes from Greek and Latin words meaning 'many small folds.' It may also be called cortical dysplasia or malformation of cortical develop

At what age does Polymicrogyria typically begin?

Typical onset of Polymicrogyria is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Polymicrogyria?

3 specialists and care centers treating Polymicrogyria are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.