Plastic bronchitis

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1FDA treatments8Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Plastic bronchitis is a rare and serious lung condition where thick, rubbery plugs or casts form inside the airways (bronchi) of the lungs. These casts are made of mucus, proteins, and other materials that harden and take the exact shape of the breathing tubes. Unlike normal mucus that can be coughed up easily, these casts are tough and sticky, making it very hard to breathe. The condition is also sometimes called bronchial cast disease or fibrinous bronchitis. The casts can partially or completely block the airways, causing sudden and severe breathing problems. People with plastic bronchitis often experience repeated episodes of coughing up these rubbery plugs, along with wheezing, chest tightness, and shortness of breath. In some cases, a blocked airway can cause a lung to partially collapse, which is a medical emergency. Plastic bronchitis can occur in both children and adults. It is often linked to other underlying conditions, including congenital heart disease (especially after a surgery called the Fontan procedure), lymphatic disorders, asthma, or infections. Treatment focuses on clearing the airways, managing the underlying cause, and preventing new casts from forming. Options include airway clearance therapy, inhaled medications, and in some cases, procedures to directly remove the casts. Research into better treatments is ongoing, and care from a specialized team is very important.

Also known as:

Key symptoms:

Coughing up thick, rubbery plugs or casts from the airwaysShortness of breath, sometimes sudden and severeWheezing or noisy breathingChest tightness or chest painPersistent cough that does not go awayRepeated lung infections or pneumoniaPartial lung collapse (atelectasis)Low oxygen levels in the bloodFatigue and low energyBluish tint to the lips or fingertips (cyanosis) during severe episodes

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

1 available

Acetylcysteine

ACETYLCYSTEINE· Hospira, Inc.

adjuvant therapy for patients with abnormal, viscid, or inspissated mucous secretions in emphysema with bronchitis

No actively recruiting trials found for Plastic bronchitis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Plastic bronchitis community →

Specialists

8 foundView all specialists →
KP
Kathleen A Stringer, PharmD
CHARLESTON, SC
Specialist
PI on 1 active trial
VP
Vibeke E Hjortdal, Professor
Specialist
PI on 1 active trial
MD
Michael Rahbek Schmidt, Ass. professor, PhD, DMSc
Specialist
PI on 1 active trial
WM
William Clarke, MD, MS
Specialist
PI on 1 active trial
JM
Jake Scott, MD
Specialist
PI on 1 active trial
TM
Todd Gudausky, MD
MILWAUKEE, WI
Specialist
PI on 1 active trial
BM
Bruce K Rubin, MEngr
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Plastic bronchitis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Plastic bronchitis

No recent news articles for Plastic bronchitis.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is causing my plastic bronchitis, and can that underlying cause be treated?,What airway clearance techniques or devices are best for my situation?,Which inhaled medications should I use, and how do I use them correctly?,What are the warning signs that I need to go to the emergency room immediately?,Is there a specialized center for lymphatic or cardiac interventions that might help my case?,Are there any clinical trials or new treatments I should know about?,How often should I have follow-up appointments, and what monitoring tests do I need?

Common questions about Plastic bronchitis

What is Plastic bronchitis?

Plastic bronchitis is a rare and serious lung condition where thick, rubbery plugs or casts form inside the airways (bronchi) of the lungs. These casts are made of mucus, proteins, and other materials that harden and take the exact shape of the breathing tubes. Unlike normal mucus that can be coughed up easily, these casts are tough and sticky, making it very hard to breathe. The condition is also sometimes called bronchial cast disease or fibrinous bronchitis. The casts can partially or completely block the airways, causing sudden and severe breathing problems. People with plastic bronchitis

How is Plastic bronchitis inherited?

Plastic bronchitis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Plastic bronchitis?

8 specialists and care centers treating Plastic bronchitis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.