Penile agenesis

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18Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Penile agenesis, also called aphallia or penile aplasia, is a very rare condition where a baby is born without a penis. This happens when the penis does not form properly during early pregnancy, usually between weeks 3 and 6 of fetal development. The condition affects genetic males (those with XY chromosomes), though the external appearance at birth may look different from a typical male. The urethra, which is the tube that carries urine out of the body, is usually present but opens in an abnormal location, often near the rectum or perineum. The testes may be present but are often undescended, meaning they have not moved into their normal position. Because of the way the body looks at birth, many children with penile agenesis have historically been raised as girls, though this practice is now being reconsidered in favor of more individualized, patient-centered care. Associated problems can include kidney and urinary tract abnormalities, and sometimes issues with other organs. Treatment is complex and involves a team of specialists. Surgical options exist to help with urinary function and, in some cases, to create genital structures. Hormone therapy and psychological support are also important parts of care. Decisions about gender assignment and surgical intervention are deeply personal and are now made collaboratively with families and, as the child grows, with the patient themselves.

Also known as:

Key symptoms:

Absent penis at birthUrethra opening in an abnormal location, such as near the rectum or perineumUndescended testes (testes not in their normal position)Difficulty or abnormal pattern of urinationPossible kidney or urinary tract abnormalitiesPossible abnormalities of the scrotumAmbiguous or atypical genital appearance at birth

Clinical phenotype terms (29)— hover any for plain English
Abnormality of the bladderHP:0000014Urethral atresia, maleHP:0000052HydroureterHP:0000072Cystic renal dysplasiaHP:0000800Bilateral talipes equinovarusHP:0001776Bilateral lung agenesisHP:0005944Atrophy of the spinal cordHP:0006827Maternal diabetesHP:0009800
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

3 events
Jun 2025Pilot Study of PEnile TRAnsplantation - Vascularized Composite Allografts

Hospices Civils de Lyon — NA

TrialNOT YET RECRUITING
Sep 2024Comparison of the Effect of Testosterone Administered for Micropenis Hypospadias Surgery With Bispectral Index

Namik Kemal University

TrialNOT YET RECRUITING
Jun 2014Human Penile Allotransplantation

Johns Hopkins University — PHASE2, PHASE3

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Penile agenesis.

View clinical trials →

No actively recruiting trials found for Penile agenesis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Penile agenesis community →

Specialists

18 foundView all specialists →
BC
Bruno Nicolino Cezarino
Specialist
1 Penile agenesis publication
OB
Oumnia Bencharef
Specialist
1 Penile agenesis publication
KF
Karima Fouraiji
Specialist
1 Penile agenesis publication
EK
El Ouafi El Aouni Kamili
Specialist
1 Penile agenesis publication
MS
Mohamed Oulad Saiad
Specialist
1 Penile agenesis publication
CA
Collins Chijioke Adumah
Specialist
1 Penile agenesis publication
IA
Iniofon Clement Akpaette
Specialist
1 Penile agenesis publication
OO
Owolabi Oni
Specialist
1 Penile agenesis publication
IO
Igwe Arua Obasi
Specialist
1 Penile agenesis publication
IO
Ibukunolu Olufemi Ogundele
Specialist
1 Penile agenesis publication
AA
Abdulhafiz Adesunkanmi
Specialist
1 Penile agenesis publication
OO
Oluwaseun Abioye Oyinloye
Specialist
1 Penile agenesis publication
AT
Ademola Olusegun Talabi
Specialist
1 Penile agenesis publication
OS
Oludayo Adedapo Sowande
Specialist
1 Penile agenesis publication
OA
Olusanya Adejuyigbe
Specialist
1 Penile agenesis publication
NM
Nelly Pitteloud, M.D.
BOSTON, MA
Specialist
PI on 1 active trial
RM
Richard Redett, MD
BALTIMORE, MD
Specialist
PI on 1 active trial
DD
Dae Yul Yang, Director
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Penile agenesis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Penile agenesis

Disease timeline:

New recruiting trial: Human Penile Allotransplantation

A new clinical trial is recruiting patients for Penile agenesis

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What tests do we need to do right away to make sure my child's kidneys and urinary tract are healthy?,What are the surgical options available, and when would you recommend them?,How should we approach decisions about gender assignment, and what does current evidence say?,What psychological support is available for our child and our family?,Are there any associated conditions or syndromes we should be tested for?,What does long-term follow-up look like, and which specialists will be involved?,Are there patient or family support groups you would recommend for families dealing with this condition?

Common questions about Penile agenesis

What is Penile agenesis?

Penile agenesis, also called aphallia or penile aplasia, is a very rare condition where a baby is born without a penis. This happens when the penis does not form properly during early pregnancy, usually between weeks 3 and 6 of fetal development. The condition affects genetic males (those with XY chromosomes), though the external appearance at birth may look different from a typical male. The urethra, which is the tube that carries urine out of the body, is usually present but opens in an abnormal location, often near the rectum or perineum. The testes may be present but are often undescended,

How is Penile agenesis inherited?

Penile agenesis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Penile agenesis typically begin?

Typical onset of Penile agenesis is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Penile agenesis?

18 specialists and care centers treating Penile agenesis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.