Paramedian facial cleft

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Overview

Paramedian facial cleft is a very rare birth defect where there is an abnormal gap or split in the face that runs alongside (but not exactly in) the midline of the face. This condition is present at birth and results from incomplete fusion of the facial structures during early development in the womb. The cleft can affect the upper lip, nose, and sometimes the area between the nose and the eye. The severity varies widely — some individuals have a subtle notch or groove, while others have a more obvious gap that can involve the skin, underlying bone, and soft tissues of the face. Paramedian facial clefts are classified within the Tessier classification system for craniofacial clefts, which helps surgeons and doctors describe the exact location and extent of the cleft. These clefts can occur in isolation or as part of a broader syndrome involving other birth defects. Affected individuals may have difficulty with breathing, feeding, speech, and facial appearance. Treatment is primarily surgical and often requires a team of specialists. Reconstructive surgery aims to close the cleft, restore normal facial structure, and improve function. Multiple surgeries may be needed over the course of childhood and adolescence. Speech therapy, dental care, and psychological support are also important parts of the overall treatment plan. Early intervention leads to the best outcomes for both function and appearance.

Also known as:

Key symptoms:

Visible gap or split in the face near the midlineCleft or notch in the upper lipAbnormal shape or structure of the noseWidely spaced eyes or abnormal eye positionDifficulty feeding as a newbornBreathing difficultiesSpeech problemsDental abnormalities or missing teethUnderdeveloped facial bonesAsymmetry of the facePossible involvement of the eye areaScarring or skin irregularities along the cleft

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Paramedian facial cleft.

View clinical trials →

No actively recruiting trials found for Paramedian facial cleft at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Paramedian facial cleft community →

No specialists are currently listed for Paramedian facial cleft.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Paramedian facial cleft.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Paramedian facial cleft

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of facial cleft does my child have, and how severe is it?,Is this cleft part of a larger syndrome, and should we do genetic testing?,How many surgeries will my child likely need, and when should the first one happen?,What feeding strategies should we use before surgery?,Will my child need speech therapy, and when should it start?,What are the expected cosmetic and functional outcomes after surgery?,Are there any support groups or resources for families dealing with craniofacial conditions?

Common questions about Paramedian facial cleft

What is Paramedian facial cleft?

Paramedian facial cleft is a very rare birth defect where there is an abnormal gap or split in the face that runs alongside (but not exactly in) the midline of the face. This condition is present at birth and results from incomplete fusion of the facial structures during early development in the womb. The cleft can affect the upper lip, nose, and sometimes the area between the nose and the eye. The severity varies widely — some individuals have a subtle notch or groove, while others have a more obvious gap that can involve the skin, underlying bone, and soft tissues of the face. Paramedian fa

At what age does Paramedian facial cleft typically begin?

Typical onset of Paramedian facial cleft is neonatal. Age of onset can vary across affected individuals.