Otopalatodigital syndrome spectrum disorder

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3Specialists8Treatment centers1Financial resources

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Otopalatodigital syndrome spectrum disorder (OPD spectrum disorder) is a group of rare genetic conditions that affect the development of bones and other body structures. This spectrum includes several related conditions: otopalatodigital syndrome type 1 (OPD1), otopalatodigital syndrome type 2 (OPD2), frontometaphyseal dysplasia (FMD), Melnick-Needles syndrome (MNS), and terminal osseous dysplasia with pigmentary defects (TODPD). The name 'otopalatodigital' refers to the three main areas affected: the ears (oto), the roof of the mouth or palate (palato), and the fingers and toes (digital). People with OPD spectrum disorders may have hearing loss, a cleft palate or a highly arched palate, and bone abnormalities in the fingers, toes, and other parts of the skeleton. Facial features may appear distinctive, including a prominent brow ridge and wide-set eyes. The severity varies widely across the spectrum. OPD1 tends to be milder, while OPD2 can be very severe and sometimes life-threatening in newborn males. There is currently no cure for OPD spectrum disorders. Treatment focuses on managing symptoms and may include surgery for cleft palate or bone abnormalities, hearing aids for hearing loss, physical therapy, and supportive care. A team of specialists is usually needed to address the many body systems that can be involved.

Also known as:

Key symptoms:

Hearing loss or deafnessCleft palate or highly arched palateShort or curved fingers and toesProminent brow ridgeWide-set eyesShort statureBowing of long bonesUnderdeveloped or abnormal ribsDifficulty breathing in severe casesFeeding difficulties in infancyDistinctive facial featuresJoint stiffness or limited movementScoliosis or other spine abnormalitiesIntellectual disability (in some forms)Skin pigmentation changes (in TODPD)

Inheritance

X-linked dominant

Carried on the X chromosome; a single copy can cause the condition

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

3 events
Dec 2023Hyperbaric Oxygen Treatment (HBOT) During Methadone Tapering

Washington State University — PHASE1

TrialACTIVE NOT RECRUITING
Jan 2023Buprenorphine Integration Research and Community Health

Yale University — NA

TrialACTIVE NOT RECRUITING
Nov 2020A Study Comparing Oral Buprenorphine and Injectable Buprenorphine for the Treatment of Opioid Use Disorder

VA Office of Research and Development — PHASE4

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Otopalatodigital syndrome spectrum disorder.

View clinical trials →

No actively recruiting trials found for Otopalatodigital syndrome spectrum disorder at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Otopalatodigital syndrome spectrum disorder community →

Specialists

3 foundView all specialists →
LM
Layton Matt, MD
Spokane, Washington
Specialist

Rare Disease Specialist

1 Otopalatodigital syndrome spectrum disorder publication
FM
Frederick L Altice, MD
Morgantown, West Virginia
Specialist

Rare Disease Specialist

PI on 4 active trials
IM
Ismene L. Petrakis, MD
Tuscaloosa, Alabama
Specialist

Rare Disease Specialist

1 Otopalatodigital syndrome spectrum disorder publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Financial Resources

1 resources

Suboxone

Indivior

Opioid Use Disorder

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copay card
Copay CardPatient Assistance
Accepting applications

Travel Grants

No travel grants are currently matched to Otopalatodigital syndrome spectrum disorder.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Otopalatodigital syndrome spectrum disorder

Disease timeline:

New trial: Buprenorphine Integration Research and Community Health

Phase NA trial recruiting. NIATx Coaching

New trial: Hyperbaric Oxygen Treatment (HBOT) During Methadone Tapering

Phase PHASE1 trial recruiting. Hyperbaric Oxygen Treatment Full

New trial: A Study Comparing Oral Buprenorphine and Injectable Buprenorphine for the Treatment of Opioid Use Di

Phase PHASE4 trial recruiting. Sublingual buprenorphine with naloxone

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which specific condition within the OPD spectrum does my child have, and what does that mean for their future?,How often should hearing be tested, and what hearing support options are available?,Will my child need surgery for bone or palate problems, and when is the best time?,What therapies (physical, speech, occupational) should we start, and how often?,Is genetic counseling recommended for our family, and what is the chance of this happening in future pregnancies?,Are there any clinical trials or new research studies we should know about?,What emergency signs should I watch for, and when should I go to the hospital?

Common questions about Otopalatodigital syndrome spectrum disorder

What is Otopalatodigital syndrome spectrum disorder?

Otopalatodigital syndrome spectrum disorder (OPD spectrum disorder) is a group of rare genetic conditions that affect the development of bones and other body structures. This spectrum includes several related conditions: otopalatodigital syndrome type 1 (OPD1), otopalatodigital syndrome type 2 (OPD2), frontometaphyseal dysplasia (FMD), Melnick-Needles syndrome (MNS), and terminal osseous dysplasia with pigmentary defects (TODPD). The name 'otopalatodigital' refers to the three main areas affected: the ears (oto), the roof of the mouth or palate (palato), and the fingers and toes (digital). Pe

How is Otopalatodigital syndrome spectrum disorder inherited?

Otopalatodigital syndrome spectrum disorder follows a x-linked dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Otopalatodigital syndrome spectrum disorder typically begin?

Typical onset of Otopalatodigital syndrome spectrum disorder is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Otopalatodigital syndrome spectrum disorder?

3 specialists and care centers treating Otopalatodigital syndrome spectrum disorder are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.

What treatment and support options exist for Otopalatodigital syndrome spectrum disorder?

1 patient support program are currently tracked on UniteRare for Otopalatodigital syndrome spectrum disorder. See the treatments and support programs sections for copay assistance, eligibility, and contact details.