Orofaciodigital syndrome type 8

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ORPHA:2755OMIM:300484Q87.0
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Overview

Orofaciodigital syndrome type 8 (OFD8), also known as Edwards syndrome or Orofaciodigital syndrome type VIII, is an extremely rare genetic condition that affects the mouth (oral), face (facial), and fingers and toes (digital). It belongs to a larger group of conditions called orofaciodigital syndromes, of which there are multiple types. OFD8 is specifically characterized by abnormalities of the tongue, teeth, and other structures in the mouth, along with facial differences and extra fingers or toes (polydactyly). Some individuals may also have tibial abnormalities, meaning the shinbone may be shortened or underdeveloped. Intellectual disability has been reported in some cases but is not always present. Because OFD8 is so rare, with only a handful of cases described in the medical literature, our understanding of the full range of symptoms and the best approaches to treatment is still limited. There is currently no cure for OFD8. Treatment focuses on managing individual symptoms, which may include surgery to correct extra digits, dental care for oral abnormalities, and supportive therapies such as speech therapy or physical therapy. A team of specialists is usually needed to provide comprehensive care. Early diagnosis and intervention can help improve quality of life for affected individuals and their families.

Also known as:

Key symptoms:

Extra fingers or toes (polydactyly)Abnormalities of the tongue, such as lobulated or split tongueDental abnormalities including missing or extra teethCleft lip or cleft palateShort or underdeveloped shinbone (tibial deficiency)Facial asymmetry or unusual facial featuresSmall jaw (micrognathia)Widely spaced eyesShort statureIntellectual disability in some casesSpeech difficultiesHearing problemsAbnormal frenula (small folds of tissue in the mouth)

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Orofaciodigital syndrome type 8.

View clinical trials →

No actively recruiting trials found for Orofaciodigital syndrome type 8 at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Orofaciodigital syndrome type 8 community →

No specialists are currently listed for Orofaciodigital syndrome type 8.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Orofaciodigital syndrome type 8.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Orofaciodigital syndrome type 8

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features of OFD8 does my child have, and how severe are they?,Is genetic testing available to confirm the diagnosis and identify the exact cause?,What surgeries or procedures will my child need, and when should they be done?,Will my child need speech therapy, physical therapy, or other supportive services?,What is the chance of having another child with this condition?,Are there any clinical studies or research programs we could participate in?,How often should my child be seen by each specialist?

Common questions about Orofaciodigital syndrome type 8

What is Orofaciodigital syndrome type 8?

Orofaciodigital syndrome type 8 (OFD8), also known as Edwards syndrome or Orofaciodigital syndrome type VIII, is an extremely rare genetic condition that affects the mouth (oral), face (facial), and fingers and toes (digital). It belongs to a larger group of conditions called orofaciodigital syndromes, of which there are multiple types. OFD8 is specifically characterized by abnormalities of the tongue, teeth, and other structures in the mouth, along with facial differences and extra fingers or toes (polydactyly). Some individuals may also have tibial abnormalities, meaning the shinbone may be

How is Orofaciodigital syndrome type 8 inherited?

Orofaciodigital syndrome type 8 follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Orofaciodigital syndrome type 8 typically begin?

Typical onset of Orofaciodigital syndrome type 8 is neonatal. Age of onset can vary across affected individuals.