OBSOLETE: Tricho-oculo-dermo-vertebral syndrome

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Overview

Tricho-oculo-dermo-vertebral syndrome (also known as TODV syndrome or Alves syndrome) is an extremely rare genetic condition that affects multiple body systems. The name describes the main areas involved: 'tricho' refers to hair abnormalities, 'oculo' refers to eye problems, 'dermo' refers to skin findings, and 'vertebral' refers to spine or bone abnormalities. Note that this condition has been classified as 'obsolete' in some medical databases, meaning it may have been reclassified or merged with another diagnosis as medical understanding has advanced. Patients with this syndrome may be born with sparse or abnormal hair, eye abnormalities (such as small eyes or other structural eye problems), skin findings (including abnormal patches or unusual skin texture), and vertebral or spinal defects. Some patients may also have facial differences and other developmental features. Because so few cases have been reported in the medical literature, the full range of symptoms and their severity is not completely understood. There is currently no cure for this condition. Treatment focuses on managing individual symptoms. This may include eye care from an ophthalmologist, orthopedic management for spinal issues, dermatological care for skin problems, and supportive therapies as needed. Because the condition is so rare, care is typically coordinated by a clinical geneticist who can help guide the involvement of multiple specialists.

Also known as:

Key symptoms:

Sparse or abnormal hairSmall or abnormally shaped eyesVision problemsSkin abnormalities or unusual skin patchesSpine or vertebral defectsFacial differencesShort statureAbnormal eyelashes or eyebrowsSkeletal abnormalitiesPossible hearing difficulties

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Tricho-oculo-dermo-vertebral syndrome.

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No actively recruiting trials found for OBSOLETE: Tricho-oculo-dermo-vertebral syndrome at this time.

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Search ClinicalTrials.gov ↗Join the OBSOLETE: Tricho-oculo-dermo-vertebral syndrome community →

No specialists are currently listed for OBSOLETE: Tricho-oculo-dermo-vertebral syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Tricho-oculo-dermo-vertebral syndrome.

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Community

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Latest news about OBSOLETE: Tricho-oculo-dermo-vertebral syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features of this syndrome does my child have, and how severe are they?,How often should we schedule eye exams and spine check-ups?,Are there any genetic tests that could help confirm the diagnosis or identify the cause?,What therapies or interventions are recommended for the spinal abnormalities?,Should we consider genetic counseling for future family planning?,Are there any other conditions we should rule out that look similar to this syndrome?,What resources or support groups are available for families affected by this condition?

Common questions about OBSOLETE: Tricho-oculo-dermo-vertebral syndrome

What is OBSOLETE: Tricho-oculo-dermo-vertebral syndrome?

Tricho-oculo-dermo-vertebral syndrome (also known as TODV syndrome or Alves syndrome) is an extremely rare genetic condition that affects multiple body systems. The name describes the main areas involved: 'tricho' refers to hair abnormalities, 'oculo' refers to eye problems, 'dermo' refers to skin findings, and 'vertebral' refers to spine or bone abnormalities. Note that this condition has been classified as 'obsolete' in some medical databases, meaning it may have been reclassified or merged with another diagnosis as medical understanding has advanced. Patients with this syndrome may be born

How is OBSOLETE: Tricho-oculo-dermo-vertebral syndrome inherited?

OBSOLETE: Tricho-oculo-dermo-vertebral syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does OBSOLETE: Tricho-oculo-dermo-vertebral syndrome typically begin?

Typical onset of OBSOLETE: Tricho-oculo-dermo-vertebral syndrome is neonatal. Age of onset can vary across affected individuals.