OBSOLETE: Syndromes with synostoses of limbs

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ORPHA:294961
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1Active trials8Treatment centers

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Overview

"Syndromes with synostoses of limbs" is an obsolete (no longer actively used) grouping term from the Orphanet rare disease classification system. It was used to describe a collection of rare genetic conditions in which bones in the arms, legs, hands, or feet become abnormally fused together. The medical term "synostosis" means the joining or fusion of two or more bones that are normally separate. This fusion can happen before birth during development or progress during childhood. It can affect fingers, toes, forearm bones, or other limb bones, and may limit movement and function of the affected joints. Because this is an obsolete umbrella category rather than a single specific disease, the conditions that were once grouped here have since been reclassified into more specific diagnoses. Examples include conditions like multiple synostoses syndrome, proximal symphalangism, tarsal-carpal coalition syndrome, and other skeletal dysplasias involving bone fusion. Each of these specific conditions has its own genetic cause, inheritance pattern, and clinical features. If you or your child has been given a diagnosis that falls under this older category, it is important to work with a clinical geneticist to identify the specific underlying condition. A precise diagnosis will help guide treatment, genetic counseling, and long-term management. Treatment for bone fusion syndromes is generally supportive and may include surgery to improve joint movement, physical therapy, and pain management. There are currently no cures for these genetic skeletal conditions, but care can significantly improve quality of life.

Key symptoms:

Fusion of bones in the hands or feetStiff or immovable jointsLimited range of motion in arms or legsFused fingers or toesShort fingers or toesDifficulty gripping or grasping objectsPain in affected jointsAbnormal walking or gaitHearing loss in some subtypesForearm bones fused togetherDifficulty with fine motor tasksSkeletal deformities visible on X-ray

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
Sep 2025Surgical Corection of Congenital Proximal Radioulnar Synostosis Using Double Osteotomy Technique.

Sohag University — NA

TrialNOT YET RECRUITING
Sep 2022Comparing Conservative to Surgical Treatment of Trigonocephaly Craniofacial Surgery in Children With Trigonocephaly: an Observational Cohort Study on Clinical Outcomes, Psychosocial Wellbeing, and Costs

Erasmus Medical Center

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Syndromes with synostoses of limbs.

1 clinical trialare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

1 recruitingView all trials with filters →
Other1 trial
Comparing Conservative to Surgical Treatment of Trigonocephaly Craniofacial Surgery in Children With Trigonocephaly: an Observational Cohort Study on Clinical Outcomes, Psychosocial Wellbeing, and Costs
Actively Recruiting
PI: Irene MJ Mathijssen, MD, PhD, MBA-H (Erasmus Medical Center) · Sites: Rotterdam, ROTTERDAM · Age: 08 yrs

No specialists are currently listed for OBSOLETE: Syndromes with synostoses of limbs.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Syndromes with synostoses of limbs.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the specific syndrome causing the bone fusions in my child or me?,Which gene is responsible, and what does genetic testing show?,Will the bone fusions get worse over time?,Would surgery help improve joint movement, and what are the risks?,What therapies can help maintain function in daily activities?,Is there a risk of passing this condition to future children?,Are there any other organs or systems I should be monitored for?

Common questions about OBSOLETE: Syndromes with synostoses of limbs

What is OBSOLETE: Syndromes with synostoses of limbs?

"Syndromes with synostoses of limbs" is an obsolete (no longer actively used) grouping term from the Orphanet rare disease classification system. It was used to describe a collection of rare genetic conditions in which bones in the arms, legs, hands, or feet become abnormally fused together. The medical term "synostosis" means the joining or fusion of two or more bones that are normally separate. This fusion can happen before birth during development or progress during childhood. It can affect fingers, toes, forearm bones, or other limb bones, and may limit movement and function of the affecte

At what age does OBSOLETE: Syndromes with synostoses of limbs typically begin?

Typical onset of OBSOLETE: Syndromes with synostoses of limbs is neonatal. Age of onset can vary across affected individuals.

Are there clinical trials for OBSOLETE: Syndromes with synostoses of limbs?

Yes — 1 recruiting clinical trial is currently listed for OBSOLETE: Syndromes with synostoses of limbs on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.