OBSOLETE: Split hand

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:294992
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Split hand, also known as ectrodactyly or split hand/foot malformation (SHFM), is a congenital limb condition present at birth in which the middle fingers or toes are missing, giving the hand or foot a cleft or "V-shaped" appearance. The condition can range from mild (with only a small notch or missing finger) to more severe forms where several central fingers or toes are absent. It can affect one hand, both hands, one or both feet, or any combination. Split hand can occur as an isolated finding or as part of a broader genetic syndrome that may involve other parts of the body. The condition develops during early pregnancy when the hand or foot does not form properly. In many cases, split hand runs in families and follows an autosomal dominant inheritance pattern, meaning only one copy of the changed gene is needed to cause the condition. However, the severity can vary widely even within the same family — some family members may be mildly affected while others have more noticeable differences. Treatment focuses on improving hand or foot function and appearance. Surgery may be recommended to close the cleft, separate fused fingers, or improve grip. Occupational therapy and adaptive devices can help children develop fine motor skills. Many people with split hand live full, active lives with good hand function, especially with early intervention and supportive care.

Also known as:

Key symptoms:

Missing central fingers or toesV-shaped cleft in the hand or footFused fingers or toes (syndactyly)Underdeveloped or shortened fingersAbnormally shaped nailsReduced grip strengthDifficulty with fine motor tasks like buttoning clothesFeet may have missing or fused toesCondition may affect one or both handsCondition may affect one or both feet

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Split hand.

View clinical trials →

No actively recruiting trials found for OBSOLETE: Split hand at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the OBSOLETE: Split hand community →

No specialists are currently listed for OBSOLETE: Split hand.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Split hand.

Search all travel grants →NORD Financial Assistance ↗

Community

Open OBSOLETE: Split handForum →

No community posts yet. Be the first to share your experience with OBSOLETE: Split hand.

Start the conversation →

Latest news about OBSOLETE: Split hand

No recent news articles for OBSOLETE: Split hand.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of split hand/foot malformation does my child have, and what is the genetic cause?,Would surgery improve my child's hand or foot function, and when is the best time for it?,Should we pursue genetic testing, and what would the results mean for our family?,What kind of occupational therapy would benefit my child?,Are there any associated conditions or syndromes we should screen for?,What is the chance of this condition occurring in future children?,Are there support groups or resources for families affected by limb differences?

Common questions about OBSOLETE: Split hand

What is OBSOLETE: Split hand?

Split hand, also known as ectrodactyly or split hand/foot malformation (SHFM), is a congenital limb condition present at birth in which the middle fingers or toes are missing, giving the hand or foot a cleft or "V-shaped" appearance. The condition can range from mild (with only a small notch or missing finger) to more severe forms where several central fingers or toes are absent. It can affect one hand, both hands, one or both feet, or any combination. Split hand can occur as an isolated finding or as part of a broader genetic syndrome that may involve other parts of the body. The condition d

At what age does OBSOLETE: Split hand typically begin?

Typical onset of OBSOLETE: Split hand is neonatal. Age of onset can vary across affected individuals.