OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies

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ORPHA:138066
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Overview

Pierre Robin syndrome (also called Pierre Robin sequence) associated with miscellaneous anomalies is a term that was previously used to describe cases where the classic features of Pierre Robin sequence occur alongside other birth defects or developmental differences that don't fit neatly into a single recognized syndrome. Pierre Robin sequence itself involves three main features present at birth: a very small lower jaw (micrognathia), a tongue that falls back into the throat (glossoptosis), and often a gap in the roof of the mouth (cleft palate). When these features appear together with additional anomalies — such as heart defects, limb differences, eye problems, or developmental delays — doctors historically grouped them under this label. It is important to note that this specific Orphanet entry (138066) is now marked as OBSOLETE. This means the medical community has moved away from using this classification. Many cases previously grouped here have since been reclassified into more specific genetic syndromes as our understanding of the underlying causes has improved. Examples of better-defined conditions include Stickler syndrome, velocardiofacial syndrome (22q11.2 deletion syndrome), and Treacher Collins syndrome, among others. Because this is an obsolete classification, patients or families who were given this diagnosis in the past should work with a clinical geneticist to determine whether a more specific and current diagnosis can be made. Modern genetic testing can often identify the precise cause, which is important for guiding treatment, understanding the expected course of the condition, and providing accurate genetic counseling for the family.

Also known as:

Key symptoms:

Very small or receding lower jawTongue falling back into the throat causing breathing problemsOpening or gap in the roof of the mouth (cleft palate)Difficulty feeding as a newbornNoisy breathing or snoringEpisodes of breathing obstruction, especially during sleepHeart defectsLimb or hand differencesEye or vision problemsHearing lossDevelopmental delaysGrowth problemsJoint or skeletal abnormalities

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies.

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No specialists are currently listed for OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies.

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.Can genetic testing identify a more specific diagnosis for my child's condition?,How severe is my child's airway obstruction, and what is the best way to manage it?,What feeding approach do you recommend, and should we see a feeding specialist?,When should cleft palate repair surgery be planned?,What other organs or systems should be checked for associated problems?,What developmental milestones should I watch for, and when should I be concerned?,Are there any implications for future pregnancies in our family?

Common questions about OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies

What is OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies?

Pierre Robin syndrome (also called Pierre Robin sequence) associated with miscellaneous anomalies is a term that was previously used to describe cases where the classic features of Pierre Robin sequence occur alongside other birth defects or developmental differences that don't fit neatly into a single recognized syndrome. Pierre Robin sequence itself involves three main features present at birth: a very small lower jaw (micrognathia), a tongue that falls back into the throat (glossoptosis), and often a gap in the roof of the mouth (cleft palate). When these features appear together with addit

At what age does OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies typically begin?

Typical onset of OBSOLETE: Pierre Robin syndrome associated with miscellaneous anomalies is neonatal. Age of onset can vary across affected individuals.