OBSOLETE: Isolated plagiocephaly

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:35098
Who is this for?
Show terms as
2Active trials8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Isolated plagiocephaly — also called 'flat head syndrome' or positional plagiocephaly — is a condition where a baby's skull develops an asymmetrical or flattened shape. The word 'plagiocephaly' comes from Greek words meaning 'oblique head.' It is listed as 'obsolete' in some medical databases because it is now more precisely classified into subtypes, but the condition itself is still very real and commonly seen in infants. The skull of a newborn is soft and made up of several bony plates that have not yet fused together. This flexibility allows the baby's head to pass through the birth canal, but it also means the skull can be reshaped by pressure. When a baby spends a lot of time lying in the same position, or when there is pressure on the skull before or during birth, one area of the head can become flattened. This can cause the head to look uneven, with one side of the forehead or back of the skull appearing pushed forward or flat. Most cases of isolated plagiocephaly are positional (not caused by the skull bones fusing too early) and do not affect brain development. Treatment usually involves repositioning techniques, physical therapy, and sometimes a custom helmet or band. When caught early, the outlook is very good, and most children's heads round out significantly with treatment.

Also known as:

Key symptoms:

Flattening on one side or the back of the baby's headAsymmetrical head shape when viewed from aboveOne ear appearing further forward than the otherUneven forehead — one side may bulge slightlyFacial asymmetry, such as uneven cheeks or eye openingsBaby consistently turning head to one preferred sideTight neck muscles on one side (torticollis)Difficulty turning the head fully in both directions

Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
Aug 2024Monitoring System for Cranial Orthoses

University of Texas Southwestern Medical Center

TrialRECRUITING
May 2023Effectiveness of Repositioning and Cranial Remolding in Infants With Cranial Deformation

University of Texas Southwestern Medical Center — NA

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Isolated plagiocephaly.

2 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

2 recruitingView all trials with filters →
N/A1 trial
Effectiveness of Repositioning and Cranial Remolding in Infants With Cranial Deformation
N/A
Actively Recruiting
PI: Tiffany Graham (University of Texas Southwestern Medical Center) · Sites: Dallas, Texas
Other1 trial
Monitoring System for Cranial Orthoses
Actively Recruiting
PI: Tiffany Graham, MS (University of Texas Southwestern Medical Center) · Sites: Dallas, Texas

No specialists are currently listed for OBSOLETE: Isolated plagiocephaly.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Isolated plagiocephaly.

Search all travel grants →NORD Financial Assistance ↗

Community

Open OBSOLETE: Isolated plagiocephalyForum →

No community posts yet. Be the first to share your experience with OBSOLETE: Isolated plagiocephaly.

Start the conversation →

Latest news about OBSOLETE: Isolated plagiocephaly

No recent news articles for OBSOLETE: Isolated plagiocephaly.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is my baby's flat head positional, or could it be caused by the skull bones fusing too early (craniosynostosis)?,Does my baby need a helmet, or can repositioning and physical therapy be enough?,At what age is helmet therapy most effective, and is my baby still in that window?,How do I know if the physical therapy exercises are working?,Will there be any lasting effects on my child's appearance or brain development?,How often do we need follow-up appointments to track progress?,Are there any signs I should watch for that would mean we need to come in sooner?

Common questions about OBSOLETE: Isolated plagiocephaly

What is OBSOLETE: Isolated plagiocephaly?

Isolated plagiocephaly — also called 'flat head syndrome' or positional plagiocephaly — is a condition where a baby's skull develops an asymmetrical or flattened shape. The word 'plagiocephaly' comes from Greek words meaning 'oblique head.' It is listed as 'obsolete' in some medical databases because it is now more precisely classified into subtypes, but the condition itself is still very real and commonly seen in infants. The skull of a newborn is soft and made up of several bony plates that have not yet fused together. This flexibility allows the baby's head to pass through the birth canal,

How is OBSOLETE: Isolated plagiocephaly inherited?

OBSOLETE: Isolated plagiocephaly follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does OBSOLETE: Isolated plagiocephaly typically begin?

Typical onset of OBSOLETE: Isolated plagiocephaly is neonatal. Age of onset can vary across affected individuals.

Are there clinical trials for OBSOLETE: Isolated plagiocephaly?

Yes — 2 recruiting clinical trials are currently listed for OBSOLETE: Isolated plagiocephaly on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.