OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome

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ORPHA:171860
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Overview

Intellectual disability-cataracts-kyphosis syndrome is an extremely rare condition that has been described in medical literature but is now considered an obsolete diagnostic category in Orphanet, meaning it may have been reclassified, merged with another condition, or found to not represent a distinct disease entity. As the name suggests, the syndrome was originally characterized by a combination of intellectual disability (difficulty with learning and reasoning), cataracts (clouding of the lens of the eye leading to vision problems), and kyphosis (an abnormal forward rounding of the upper back or spine). These three features together were thought to define a unique syndrome. Because this condition has been marked as obsolete, patients who were previously diagnosed with this syndrome may now fall under a different or updated diagnosis. If you or a family member received this diagnosis, it is important to consult with a clinical geneticist who can review the case with current knowledge and potentially reclassify the condition. Treatment has generally been supportive, focusing on managing each symptom individually — such as surgery for cataracts, physical therapy or bracing for kyphosis, and educational support for intellectual disability.

Key symptoms:

Intellectual disability or learning difficultiesCataracts (cloudy lenses in the eyes)Kyphosis (rounded or hunched upper back)Delayed developmental milestonesVision problems or blurry visionBack pain or stiffnessDifficulty with daily tasks requiring reasoning

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome.

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No actively recruiting trials found for OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome at this time.

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No specialists are currently listed for OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome.

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Community

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Latest news about OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Since this diagnosis is now considered obsolete, does my condition fit a currently recognized syndrome?,Would genetic testing help identify a more specific diagnosis?,What is the best treatment plan for the cataracts — is surgery recommended now or should we wait?,How should we monitor and manage the kyphosis over time?,What educational and developmental support services are available?,Are there any clinical trials or research studies that might be relevant?,What specialists should be part of the ongoing care team?

Common questions about OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome

What is OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome?

Intellectual disability-cataracts-kyphosis syndrome is an extremely rare condition that has been described in medical literature but is now considered an obsolete diagnostic category in Orphanet, meaning it may have been reclassified, merged with another condition, or found to not represent a distinct disease entity. As the name suggests, the syndrome was originally characterized by a combination of intellectual disability (difficulty with learning and reasoning), cataracts (clouding of the lens of the eye leading to vision problems), and kyphosis (an abnormal forward rounding of the upper bac

At what age does OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome typically begin?

Typical onset of OBSOLETE: Intellectual disability-cataracts-kyphosis syndrome is childhood. Age of onset can vary across affected individuals.