OBSOLETE: Humero-radio-ulnar synostosis, bilateral

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Overview

Humero-radio-ulnar synostosis, bilateral, is an extremely rare skeletal condition in which the bones of the upper arm (humerus) and the two forearm bones (radius and ulna) are abnormally fused together on both sides of the body. The term 'synostosis' means that bones that are normally separate have grown together, which limits or completely prevents movement at the elbow joint. Because this entry is marked as 'OBSOLETE' in the Orphanet classification system, it means the condition has likely been reclassified or merged into a broader diagnostic category, such as a more general radio-ulnar synostosis syndrome or another skeletal dysplasia. Patients with this condition typically notice significant stiffness or complete inability to bend, straighten, or rotate the elbows and forearms. This can make everyday tasks like eating, dressing, and reaching very difficult. The condition is usually present from birth, as the fusion occurs during fetal development. Treatment is mainly supportive and may include physical therapy, occupational therapy, adaptive devices, and in some cases surgery to try to improve range of motion. Because this is a very rare condition, management is best guided by specialists experienced in skeletal abnormalities.

Also known as:

Key symptoms:

Inability to bend or straighten the elbowsInability to rotate the forearms (turning palms up or down)Stiff or locked elbow joints on both sidesDifficulty with self-care tasks like eating and dressingLimited arm movement from birthForearms fixed in one positionDifficulty reaching overheadPossible abnormal arm posture

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Humero-radio-ulnar synostosis, bilateral.

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No actively recruiting trials found for OBSOLETE: Humero-radio-ulnar synostosis, bilateral at this time.

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No specialists are currently listed for OBSOLETE: Humero-radio-ulnar synostosis, bilateral.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Humero-radio-ulnar synostosis, bilateral.

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Community

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Latest news about OBSOLETE: Humero-radio-ulnar synostosis, bilateral

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is this condition part of a broader genetic syndrome, or is it isolated?,Would genetic testing help us understand the cause or risk for future children?,What surgical options exist to improve arm function?,What position are the arms fixed in, and how does that affect what my child can do?,What types of occupational therapy and adaptive devices would be most helpful?,Are there any clinical trials or research studies we could participate in?,How can we best support our child's independence at school and at home?

Common questions about OBSOLETE: Humero-radio-ulnar synostosis, bilateral

What is OBSOLETE: Humero-radio-ulnar synostosis, bilateral?

Humero-radio-ulnar synostosis, bilateral, is an extremely rare skeletal condition in which the bones of the upper arm (humerus) and the two forearm bones (radius and ulna) are abnormally fused together on both sides of the body. The term 'synostosis' means that bones that are normally separate have grown together, which limits or completely prevents movement at the elbow joint. Because this entry is marked as 'OBSOLETE' in the Orphanet classification system, it means the condition has likely been reclassified or merged into a broader diagnostic category, such as a more general radio-ulnar syno

At what age does OBSOLETE: Humero-radio-ulnar synostosis, bilateral typically begin?

Typical onset of OBSOLETE: Humero-radio-ulnar synostosis, bilateral is neonatal. Age of onset can vary across affected individuals.