OBSOLETE: Humero-radial synostosis, bilateral

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ORPHA:295211
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Overview

Humero-radial synostosis, bilateral, is an extremely rare skeletal condition in which the humerus (the upper arm bone) and the radius (one of the two forearm bones) are fused together on both sides of the body. This fusion, called synostosis, means the elbow joint cannot move normally, severely limiting the ability to bend or straighten the arms. The condition is present from birth, as the bones fail to separate properly during fetal development. It is important to note that this entry has been marked as 'OBSOLETE' in the Orphanet classification system, meaning it may have been reclassified, merged into a broader category of skeletal disorders, or redefined under a different name. Patients and families who have received this diagnosis should work with their medical team to determine the most current classification for their condition. Because the elbows are locked in a fixed position, affected individuals may have significant difficulty with everyday tasks such as feeding, dressing, and personal hygiene. Treatment is generally supportive and may include surgical intervention to attempt to restore some range of motion, physical therapy, and adaptive devices to help with daily activities. The rarity of this condition means that management is highly individualized, and outcomes depend on the severity of the fusion and whether other skeletal abnormalities are also present.

Also known as:

Key symptoms:

Inability to bend or straighten the elbowsFixed position of both armsLimited range of motion in the armsDifficulty with self-care tasks like eating and dressingAbnormal appearance of the elbow jointsPossible shortening of the forearmsDifficulty reaching the mouth or headReduced ability to carry objects

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Humero-radial synostosis, bilateral.

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No actively recruiting trials found for OBSOLETE: Humero-radial synostosis, bilateral at this time.

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No specialists are currently listed for OBSOLETE: Humero-radial synostosis, bilateral.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Humero-radial synostosis, bilateral.

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Community

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Latest news about OBSOLETE: Humero-radial synostosis, bilateral

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is this condition part of a broader genetic syndrome, or is it isolated?,Would genetic testing help us understand the cause or risk of recurrence in future children?,Is surgery an option to improve arm function, and what are the risks and expected outcomes?,What position should the arms be placed in if surgery is done to maximize daily function?,What types of occupational therapy and adaptive devices would be most helpful?,Are there other specialists we should see?,Has this diagnosis been reclassified, and what is the most current name for this condition?

Common questions about OBSOLETE: Humero-radial synostosis, bilateral

What is OBSOLETE: Humero-radial synostosis, bilateral?

Humero-radial synostosis, bilateral, is an extremely rare skeletal condition in which the humerus (the upper arm bone) and the radius (one of the two forearm bones) are fused together on both sides of the body. This fusion, called synostosis, means the elbow joint cannot move normally, severely limiting the ability to bend or straighten the arms. The condition is present from birth, as the bones fail to separate properly during fetal development. It is important to note that this entry has been marked as 'OBSOLETE' in the Orphanet classification system, meaning it may have been reclassified,

At what age does OBSOLETE: Humero-radial synostosis, bilateral typically begin?

Typical onset of OBSOLETE: Humero-radial synostosis, bilateral is neonatal. Age of onset can vary across affected individuals.