OBSOLETE: Gastric neuroendocrine tumor type 2

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Overview

Gastric neuroendocrine tumor type 2 (also called gastric NET type 2, or type 2 gastric carcinoid) is a rare type of stomach tumor that grows from special hormone-producing cells in the lining of the stomach. This condition is now considered an outdated or 'obsolete' classification in some medical coding systems, as experts have refined how these tumors are categorized. Type 2 gastric neuroendocrine tumors are closely linked to a condition called Zollinger-Ellison syndrome (ZES) combined with multiple endocrine neoplasia type 1 (MEN1), a genetic disorder that causes tumors in several hormone-producing glands. These tumors develop because too much gastrin — a hormone that tells the stomach to make acid — is produced by a separate tumor called a gastrinoma. This overload of gastrin causes the stomach's hormone cells to grow out of control, forming multiple small tumors. Symptoms often include stomach pain, acid reflux, diarrhea, and ulcers. Unlike some other stomach tumors, type 2 gastric NETs are usually slow-growing, but they can sometimes spread to other parts of the body. Treatment focuses on controlling the underlying cause — especially the gastrinoma and the excess gastrin — using medications like proton pump inhibitors and somatostatin analogs, as well as surgery when possible. Because this condition is tied to MEN1, a genetic syndrome, other family members may also be at risk and should be evaluated.

Also known as:

Key symptoms:

Stomach pain or crampingSevere acid reflux or heartburnChronic diarrheaStomach ulcers that keep coming backNausea and vomitingUnintended weight lossFeeling full quickly when eatingGastrointestinal bleeding (blood in stool or vomiting blood)FatigueSymptoms related to MEN1 such as kidney stones or low blood sugar

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Gastric neuroendocrine tumor type 2.

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No actively recruiting trials found for OBSOLETE: Gastric neuroendocrine tumor type 2 at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the OBSOLETE: Gastric neuroendocrine tumor type 2 community →

No specialists are currently listed for OBSOLETE: Gastric neuroendocrine tumor type 2.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Gastric neuroendocrine tumor type 2.

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Community

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Latest news about OBSOLETE: Gastric neuroendocrine tumor type 2

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is my tumor related to MEN1, and should my family members be tested for the MEN1 gene mutation?,What is the stage of my tumor, and has it spread anywhere in my body?,What treatment do you recommend first — medication, endoscopy, or surgery — and why?,How often will I need imaging and blood tests to monitor my condition?,Are there clinical trials available for my type of tumor?,What symptoms should prompt me to seek emergency care?,Should I see a specialist at a dedicated neuroendocrine tumor center?

Common questions about OBSOLETE: Gastric neuroendocrine tumor type 2

What is OBSOLETE: Gastric neuroendocrine tumor type 2?

Gastric neuroendocrine tumor type 2 (also called gastric NET type 2, or type 2 gastric carcinoid) is a rare type of stomach tumor that grows from special hormone-producing cells in the lining of the stomach. This condition is now considered an outdated or 'obsolete' classification in some medical coding systems, as experts have refined how these tumors are categorized. Type 2 gastric neuroendocrine tumors are closely linked to a condition called Zollinger-Ellison syndrome (ZES) combined with multiple endocrine neoplasia type 1 (MEN1), a genetic disorder that causes tumors in several hormone-pr

How is OBSOLETE: Gastric neuroendocrine tumor type 2 inherited?

OBSOLETE: Gastric neuroendocrine tumor type 2 follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does OBSOLETE: Gastric neuroendocrine tumor type 2 typically begin?

Typical onset of OBSOLETE: Gastric neuroendocrine tumor type 2 is adult. Age of onset can vary across affected individuals.