OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome

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ORPHA:1789
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Overview

Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome is an extremely rare genetic condition that was previously listed as a distinct disorder but has since been marked as obsolete in medical databases, meaning it may have been reclassified or merged with another recognized condition. The original description of this syndrome involved a combination of abnormal development of the skull and facial bones (craniofacial dysostosis), stiff or locked joints present from birth (arthrogryposis), and a facial appearance that looks prematurely aged (progeroid features). Affected individuals were noted to have distinctive facial features, limited joint movement, and skin changes that gave an older-looking appearance even in infancy or early childhood. Because this condition is obsolete in current classification systems, patients who were previously diagnosed with this syndrome may now fall under a different or updated diagnostic category. Very little published medical literature exists on this specific condition, and the exact genetic cause, inheritance pattern, and optimal management remain poorly defined. Families affected by this condition should work closely with a clinical geneticist to determine whether a more current diagnosis applies and to guide appropriate care and genetic counseling.

Also known as:

Key symptoms:

Abnormal shape of the skull and facial bonesStiff or locked joints at birthAged or old-looking facial appearance in a young childLimited range of motion in arms and legsUnusual facial featuresThin or wrinkled skinGrowth delaysSmall head sizeFeeding difficulties in infancyPossible developmental delays

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome.

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No actively recruiting trials found for OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome at this time.

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Search ClinicalTrials.gov ↗Join the OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome community →

No specialists are currently listed for OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome.

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Community

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Latest news about OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome

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Caregiver Resources

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.Since this diagnosis is now considered obsolete, what is the most current diagnosis that fits my child's symptoms?,Would whole exome or whole genome sequencing help identify the exact genetic cause?,What specialists should be part of my child's care team?,Are there any specific complications we should watch for as my child grows?,What therapies are recommended to help with joint stiffness and mobility?,Is there a risk of this condition occurring again in future pregnancies?,Are there any clinical trials or research studies that might be relevant?

Common questions about OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome

What is OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome?

Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome is an extremely rare genetic condition that was previously listed as a distinct disorder but has since been marked as obsolete in medical databases, meaning it may have been reclassified or merged with another recognized condition. The original description of this syndrome involved a combination of abnormal development of the skull and facial bones (craniofacial dysostosis), stiff or locked joints present from birth (arthrogryposis), and a facial appearance that looks prematurely aged (progeroid features). Affected individual

At what age does OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome typically begin?

Typical onset of OBSOLETE: Craniofacial dysostosis-arthrogryposis-progeroid appearance syndrome is neonatal. Age of onset can vary across affected individuals.