OBSOLETE: Congenital vascular bone syndrome with limb shortening

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ORPHA:235838
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Overview

Congenital vascular bone syndrome with limb shortening is an extremely rare condition that was previously listed in medical databases but has since been marked as obsolete, meaning it may have been reclassified, merged with another diagnosis, or determined to not represent a distinct disease entity. When it was described, this condition was thought to involve abnormalities in blood vessels (vascular malformations) that affect bone growth, leading to shortened limbs present from birth. Affected individuals may have had noticeable differences in limb length, vascular birthmarks or malformations on the skin or deeper tissues, and possible bone abnormalities visible on X-rays. Because this diagnosis is now considered obsolete, patients who were previously given this label may need to be re-evaluated by a clinical geneticist to determine whether their condition fits into a currently recognized diagnosis. Conditions that share overlapping features include Klippel-Trenaunay syndrome, Parkes Weber syndrome, and other vascular malformation syndromes that can affect bone and limb growth. Treatment would have been focused on managing symptoms, such as addressing limb length differences with orthopedic interventions and managing vascular malformations. If you or a family member received this diagnosis, it is important to seek updated genetic evaluation to ensure the most accurate and current diagnosis is applied.

Key symptoms:

Shortened arms or legs present at birthUnequal limb lengthsVisible blood vessel abnormalities on the skinBirthmarks related to blood vessel malformationsBone growth abnormalitiesSwelling in affected limbsPossible joint stiffness or limited range of motionSkin color changes over affected areas

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Congenital vascular bone syndrome with limb shortening.

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No actively recruiting trials found for OBSOLETE: Congenital vascular bone syndrome with limb shortening at this time.

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No specialists are currently listed for OBSOLETE: Congenital vascular bone syndrome with limb shortening.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Congenital vascular bone syndrome with limb shortening.

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Community

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Latest news about OBSOLETE: Congenital vascular bone syndrome with limb shortening

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Caregiver Resources

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.Since this diagnosis is now considered obsolete, what is the most current name for my condition?,Should we pursue updated genetic testing to get a more specific diagnosis?,How will my child's limb length difference be monitored and managed over time?,What are the treatment options for the vascular malformations?,Are there any clinical trials or new treatments that might apply to my condition?,What specialists should be part of my care team?,Are there any activity restrictions I should be aware of?

Common questions about OBSOLETE: Congenital vascular bone syndrome with limb shortening

What is OBSOLETE: Congenital vascular bone syndrome with limb shortening?

Congenital vascular bone syndrome with limb shortening is an extremely rare condition that was previously listed in medical databases but has since been marked as obsolete, meaning it may have been reclassified, merged with another diagnosis, or determined to not represent a distinct disease entity. When it was described, this condition was thought to involve abnormalities in blood vessels (vascular malformations) that affect bone growth, leading to shortened limbs present from birth. Affected individuals may have had noticeable differences in limb length, vascular birthmarks or malformations

At what age does OBSOLETE: Congenital vascular bone syndrome with limb shortening typically begin?

Typical onset of OBSOLETE: Congenital vascular bone syndrome with limb shortening is neonatal. Age of onset can vary across affected individuals.