OBSOLETE: Congenital myopathy with protein accumulation

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:172973
Who is this for?
Show terms as
8Treatment centers1Financial resources

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Congenital myopathy with protein accumulation is a very rare inherited muscle disorder that belongs to a group of conditions called congenital myopathies. In this condition, abnormal clumps or deposits of proteins build up inside muscle cells, which interferes with how the muscles work. This leads to muscle weakness that is usually present from birth or early infancy. The term 'OBSOLETE' in the official disease name means that this classification has been retired or merged into other, more specific diagnoses as medical understanding has improved. Patients originally diagnosed with this condition may now be reclassified under more specific types of congenital myopathy based on the particular protein that accumulates, such as myosin storage myopathy, cap myopathy, or other subtypes. The main symptoms include generalized muscle weakness, low muscle tone (floppiness), difficulty with motor milestones like sitting and walking, and sometimes breathing difficulties. The severity can range from mild weakness to more significant disability. Some patients may also experience feeding difficulties in infancy and skeletal problems such as scoliosis over time. There is currently no cure for congenital myopathies with protein accumulation. Treatment focuses on managing symptoms and may include physical therapy, respiratory support, orthopedic interventions, and nutritional support. Advances in genetic testing have helped doctors better classify these conditions, which is important for understanding prognosis and guiding care.

Key symptoms:

Muscle weakness present from birth or early lifeLow muscle tone (floppiness)Delayed motor milestones such as sitting and walkingDifficulty breathingFeeding difficulties in infancyCurved spine (scoliosis)Joint stiffness or contracturesFacial muscle weaknessFatigue and low enduranceDifficulty swallowingThin or underdeveloped musclesFrequent respiratory infections

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Congenital myopathy with protein accumulation.

View clinical trials →

No actively recruiting trials found for OBSOLETE: Congenital myopathy with protein accumulation at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the OBSOLETE: Congenital myopathy with protein accumulation community →

No specialists are currently listed for OBSOLETE: Congenital myopathy with protein accumulation.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Financial Resources

1 resources

TECENTRIQ

Genentech, Inc.

TECENTRIQ Patient Support (Genentech Access Solutions)

Patient Assistance
Manufacturer Program
Accepting applications

Travel Grants

No travel grants are currently matched to OBSOLETE: Congenital myopathy with protein accumulation.

Search all travel grants →NORD Financial Assistance ↗

Community

Open OBSOLETE: Congenital myopathy with protein accumulationForum →

No community posts yet. Be the first to share your experience with OBSOLETE: Congenital myopathy with protein accumulation.

Start the conversation →

Latest news about OBSOLETE: Congenital myopathy with protein accumulation

No recent news articles for OBSOLETE: Congenital myopathy with protein accumulation.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific subtype of congenital myopathy does my child or I have, and what gene is involved?,What is the expected course of this condition over time?,How often should breathing function be monitored?,What therapies (physical, occupational, speech) are recommended and how often?,Are there any clinical trials or emerging treatments we should know about?,What precautions should we take regarding anesthesia and surgery?,Should other family members be tested genetically?

Common questions about OBSOLETE: Congenital myopathy with protein accumulation

What is OBSOLETE: Congenital myopathy with protein accumulation?

Congenital myopathy with protein accumulation is a very rare inherited muscle disorder that belongs to a group of conditions called congenital myopathies. In this condition, abnormal clumps or deposits of proteins build up inside muscle cells, which interferes with how the muscles work. This leads to muscle weakness that is usually present from birth or early infancy. The term 'OBSOLETE' in the official disease name means that this classification has been retired or merged into other, more specific diagnoses as medical understanding has improved. Patients originally diagnosed with this conditi

At what age does OBSOLETE: Congenital myopathy with protein accumulation typically begin?

Typical onset of OBSOLETE: Congenital myopathy with protein accumulation is neonatal. Age of onset can vary across affected individuals.

What treatment and support options exist for OBSOLETE: Congenital myopathy with protein accumulation?

1 patient support program are currently tracked on UniteRare for OBSOLETE: Congenital myopathy with protein accumulation. See the treatments and support programs sections for copay assistance, eligibility, and contact details.