OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral

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ORPHA:295089
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8Treatment centers

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Overview

This condition, listed as 'Congenital absence of thigh and lower leg with foot present, unilateral,' is an extremely rare limb difference that a baby is born with. In this condition, one leg is missing the thigh (upper leg) and the lower leg (the part between the knee and ankle), but the foot is still present on that side. The other leg is normal. This means the foot is attached very close to the hip area without the usual long bones of the leg in between. This type of birth difference falls under a broader group of conditions called limb reduction defects or phocomelia-like conditions. The exact cause is often unknown, though in some cases it may be related to disruptions in blood supply during early fetal development, genetic factors, or environmental exposures during pregnancy. Because this entry is marked as 'OBSOLETE' in the Orphanet classification system, it has likely been reclassified or merged into a broader or more specific diagnostic category. Patients and families should work with their medical team to identify the most current and accurate diagnosis. Treatment typically involves a team of specialists and may include prosthetic limbs, physical therapy, and sometimes surgical procedures to improve function and mobility. Many individuals with limb differences go on to live full, active lives with appropriate support and adaptive equipment.

Also known as:

Key symptoms:

Absence of the thigh bone on one sideAbsence of the lower leg bones on one sideFoot present but attached near the hip on the affected sideSignificant leg length difference between the two sidesDifficulty with walking and standingReduced mobility without assistive devicesPossible hip joint abnormalities on the affected sideAsymmetry in body posture and balance

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral.

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No actively recruiting trials found for OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral at this time.

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No specialists are currently listed for OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact anatomy of my child's limb difference, and are there any associated conditions?,Should we pursue genetic testing to look for an underlying cause?,When should we start fitting for a prosthetic limb, and how often will it need to be replaced?,What surgical options might be considered now or in the future?,What physical therapy and rehabilitation services do you recommend?,Are there specialized limb difference clinics or multidisciplinary teams we should be referred to?,How can we connect with other families who have children with similar limb differences?

Common questions about OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral

What is OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral?

This condition, listed as 'Congenital absence of thigh and lower leg with foot present, unilateral,' is an extremely rare limb difference that a baby is born with. In this condition, one leg is missing the thigh (upper leg) and the lower leg (the part between the knee and ankle), but the foot is still present on that side. The other leg is normal. This means the foot is attached very close to the hip area without the usual long bones of the leg in between. This type of birth difference falls under a broader group of conditions called limb reduction defects or phocomelia-like conditions. The ex

How is OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral inherited?

OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral typically begin?

Typical onset of OBSOLETE: Congenital absence of thigh and lower leg with foot present, unilateral is neonatal. Age of onset can vary across affected individuals.