OBSOLETE: Autosomal dominant coarctation of aorta

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6Active trials8Treatment centers

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Overview

Autosomal dominant coarctation of aorta refers to a familial form of coarctation of the aorta, a heart condition where a section of the aorta (the large blood vessel that carries blood from the heart to the rest of the body) is abnormally narrowed. This narrowing forces the heart to work harder to pump blood through the body, which can lead to high blood pressure in the arms and upper body, while blood pressure in the legs may be lower than normal. This particular entry in medical databases is now considered obsolete, meaning it has been reclassified or merged into broader categories of congenital heart defects with autosomal dominant inheritance patterns. The condition is present from birth, though it may not be detected until later in life depending on the severity of the narrowing. Symptoms can include high blood pressure, headaches, leg cramps or cold feet, nosebleeds, and in severe cases, heart failure. In newborns, severe coarctation can be life-threatening and may require emergency treatment. Treatment typically involves surgical repair or catheter-based procedures to widen the narrowed section of the aorta. With early diagnosis and appropriate treatment, many people with coarctation of the aorta can lead relatively normal lives, though lifelong follow-up with a cardiologist is important because the condition can recur or lead to other heart problems over time. The familial (autosomal dominant) form suggests that the condition runs in families and can be passed from parent to child with a 50% chance in each pregnancy.

Key symptoms:

High blood pressure in the armsLow blood pressure or weak pulses in the legsHeadachesNosebleedsCold feet or legsLeg cramps or pain during exerciseShortness of breathChest painDizziness or faintingDifficulty feeding in infantsPoor growth in babiesHeart murmurFatigue or tiredness with physical activity

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

7 events
Jul 2025Target Organ Damage in Patients With Repaired Coarctation of Aorta and Exercise Induced Hypertension

University Medical Centre Ljubljana

TrialENROLLING BY INVITATION
Dec 2024Aortic Stiffness by CMR in Aortic Coarctation

Assiut University

TrialNOT YET RECRUITING
Aug 2024Evaluating the Feasibility of Bioresorbable Iron-Based Covered Stent: A Clinical Trial

Shubo Song — NA

TrialRECRUITING
Oct 2023The Arch Watch Study: An Integrated Evaluation of Hemodynamics in Infants With Suspected Coarctation of the Aorta

Boston Children's Hospital

TrialENROLLING BY INVITATION
Mar 2021Electronic Archive of Patients With Diagnosis and Suspected Prenatal Diagnosis of Aortic Coarctation

IRCCS Azienda Ospedaliero-Universitaria di Bologna

TrialRECRUITING
Jan 2021Growth Trial: Study of the Renata Minima Stent

Renata Medical — NA

TrialACTIVE NOT RECRUITING
Jun 2019PV Loop & Coarctation Study

University of Minnesota

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Autosomal dominant coarctation of aorta.

6 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

6 recruitingView all trials with filters →
N/A2 trials
Growth Trial: Study of the Renata Minima Stent
N/A
Active
PI: Darren Berman, MD (Children's Hospital Los Angeles) · Sites: Los Angeles, California; Los Angeles, California +5 more
Evaluating the Feasibility of Bioresorbable Iron-Based Covered Stent: A Clinical Trial
N/A
Actively Recruiting
PI: Taibing Fan, MD (Chinese Academy of Medical Sciences, Fuwai Hospita) · Sites: Zhengzhou, Henan · Age: 160 yrs
Other4 trials
PV Loop & Coarctation Study
Actively Recruiting
PI: Gurumurthy Hiremath (University of Minnesota) · Sites: Los Angeles, California; Boston, Massachusetts +5 more · Age: 699 yrs
The Arch Watch Study: An Integrated Evaluation of Hemodynamics in Infants With Suspected Coarctation of the Aorta
Enrolling by Invitation
PI: John Kheir, MD (Boston Children's Hospital) · Sites: Boston, Massachusetts
Electronic Archive of Patients With Diagnosis and Suspected Prenatal Diagnosis of Aortic Coarctation
Actively Recruiting
PI: Ylenia Bartolacelli, MD (IRCCS Azienda Ospedaliero-Universitaria di Bologna) · Sites: Bologna
Target Organ Damage in Patients With Repaired Coarctation of Aorta and Exercise Induced Hypertension
Enrolling by Invitation
· Sites: Ljubljana · Age: 1899 yrs

No specialists are currently listed for OBSOLETE: Autosomal dominant coarctation of aorta.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Autosomal dominant coarctation of aorta.

Search all travel grants →NORD Financial Assistance ↗

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Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is the coarctation, and does it need to be repaired now or can it be monitored?,What type of repair is recommended — surgery or catheter-based procedure — and what are the risks?,Should other family members be screened for coarctation or other heart defects?,What are the chances the narrowing could come back after repair?,Will my child (or I) need to take blood pressure medication long-term?,Are there any activity or exercise restrictions after treatment?,Should we pursue genetic testing to understand the familial pattern better?

Common questions about OBSOLETE: Autosomal dominant coarctation of aorta

What is OBSOLETE: Autosomal dominant coarctation of aorta?

Autosomal dominant coarctation of aorta refers to a familial form of coarctation of the aorta, a heart condition where a section of the aorta (the large blood vessel that carries blood from the heart to the rest of the body) is abnormally narrowed. This narrowing forces the heart to work harder to pump blood through the body, which can lead to high blood pressure in the arms and upper body, while blood pressure in the legs may be lower than normal. This particular entry in medical databases is now considered obsolete, meaning it has been reclassified or merged into broader categories of congen

How is OBSOLETE: Autosomal dominant coarctation of aorta inherited?

OBSOLETE: Autosomal dominant coarctation of aorta follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Are there clinical trials for OBSOLETE: Autosomal dominant coarctation of aorta?

Yes — 6 recruiting clinical trials are currently listed for OBSOLETE: Autosomal dominant coarctation of aorta on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.