Non-syndromic complete hemimelia

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Overview

Non-syndromic complete hemimelia is a rare congenital condition where a child is born with a limb that is missing its lower (or sometimes upper) segment entirely, without any other associated birth defects or underlying syndrome. The word 'hemimelia' comes from Greek meaning 'half limb.' In complete hemimelia, the affected limb is absent from a certain point downward — for example, the lower leg and foot may be completely missing while the thigh is present. 'Non-syndromic' means this occurs as an isolated finding, not as part of a broader genetic syndrome affecting multiple body systems. The condition is present at birth and is usually noticed immediately. It can affect the arms or legs, and may involve one or both sides of the body. The exact cause is not fully understood in most cases, though disruptions during early fetal limb development are believed to play a role. Some cases may be linked to genetic factors, while others appear to occur randomly. Treatment focuses on helping the child achieve the best possible function and quality of life. This typically involves prosthetic limbs, physical and occupational therapy, and sometimes surgical procedures to improve limb shape or function. With modern prosthetics and rehabilitation, many children with hemimelia grow up to lead active, independent lives.

Key symptoms:

Complete absence of the lower portion of a limb from birthMissing lower leg and/or foot (fibular or tibial hemimelia)Missing lower arm and/or hand (radial or ulnar hemimelia)Shortened or underdeveloped remaining limb segmentDifferences in limb length between the two sides of the bodyPossible differences in the shape of the remaining limb stumpDifficulty with balance and walking if a leg is affectedDifficulty with grasping or fine motor tasks if an arm is affected

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Non-syndromic complete hemimelia.

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No actively recruiting trials found for Non-syndromic complete hemimelia at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Non-syndromic complete hemimelia community →

No specialists are currently listed for Non-syndromic complete hemimelia.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Non-syndromic complete hemimelia.

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Community

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Latest news about Non-syndromic complete hemimelia

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.When is the best time to start fitting my child with a prosthetic limb, and what type is recommended?,Should we see a clinical geneticist to find out if there is a genetic cause, and what does that mean for future pregnancies?,What surgical options might be considered, and when would surgery be recommended?,How often will my child need a new prosthesis as they grow, and what does that cost?,What therapy services should my child receive, and how often?,Are there support groups or communities for children and families living with limb differences?,What signs should I watch for that would mean my child needs to be seen sooner than their next scheduled appointment?

Common questions about Non-syndromic complete hemimelia

What is Non-syndromic complete hemimelia?

Non-syndromic complete hemimelia is a rare congenital condition where a child is born with a limb that is missing its lower (or sometimes upper) segment entirely, without any other associated birth defects or underlying syndrome. The word 'hemimelia' comes from Greek meaning 'half limb.' In complete hemimelia, the affected limb is absent from a certain point downward — for example, the lower leg and foot may be completely missing while the thigh is present. 'Non-syndromic' means this occurs as an isolated finding, not as part of a broader genetic syndrome affecting multiple body systems. The

How is Non-syndromic complete hemimelia inherited?

Non-syndromic complete hemimelia follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Non-syndromic complete hemimelia typically begin?

Typical onset of Non-syndromic complete hemimelia is neonatal. Age of onset can vary across affected individuals.