Neuromuscular disease with dilated cardiomyopathy

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ORPHA:217610
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2Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Neuromuscular disease with dilated cardiomyopathy is a rare genetic condition that affects both the skeletal muscles and the heart. People with this disease experience progressive muscle weakness, which can make it harder to walk, climb stairs, or perform everyday tasks. At the same time, the heart muscle becomes stretched and weakened, a condition known as dilated cardiomyopathy. When the heart is dilated, it cannot pump blood as efficiently as it should, which can lead to heart failure symptoms such as shortness of breath, fatigue, and swelling in the legs or feet. This condition typically begins in childhood or adolescence, though the age of onset can vary. The muscle weakness usually affects the limbs and may also involve the muscles used for breathing. The heart problems can develop at the same time as the muscle weakness or may appear later. Because both the muscles and the heart are involved, this disease requires care from multiple specialists. There is currently no cure for this condition. Treatment focuses on managing symptoms and slowing disease progression. Heart medications such as ACE inhibitors, beta-blockers, and diuretics may be used to support heart function. Physical therapy and assistive devices can help maintain mobility. In severe cases of heart failure, a heart transplant may be considered. Regular monitoring of both heart and muscle function is essential for managing this disease effectively.

Key symptoms:

Progressive muscle weakness in the arms and legsEnlarged and weakened heart (dilated cardiomyopathy)Shortness of breathFatigue and low energyDifficulty walking or climbing stairsSwelling in the legs, ankles, or feetIrregular heartbeat or heart palpitationsDifficulty breathing when lying downReduced exercise toleranceMuscle wasting or loss of muscle bulkDifficulty lifting objectsBreathing difficulties due to weak respiratory muscles

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Neuromuscular disease with dilated cardiomyopathy.

View clinical trials →

No actively recruiting trials found for Neuromuscular disease with dilated cardiomyopathy at this time.

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Specialists

2 foundView all specialists →
EP
Elena Biagini, MD, PhD
Chieti, Abruzzo/Chieti
Specialist

Rare Disease Specialist

PI on 2 active trials
VP
Vlad G Zaha, MD, PhD
DALLAS, TX
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Neuromuscular disease with dilated cardiomyopathy.

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Community

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Latest news about Neuromuscular disease with dilated cardiomyopathy

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic mutation is causing this condition, and what does it mean for my prognosis?,How often should my heart function be monitored, and what tests will be needed?,What medications are recommended for my heart, and what side effects should I watch for?,Should other family members be tested for this genetic condition?,What physical activities are safe for me, and what should I avoid?,Are there any clinical trials or new treatments being studied for this condition?,When should I seek emergency medical care, and what warning signs should I look for?

Common questions about Neuromuscular disease with dilated cardiomyopathy

What is Neuromuscular disease with dilated cardiomyopathy?

Neuromuscular disease with dilated cardiomyopathy is a rare genetic condition that affects both the skeletal muscles and the heart. People with this disease experience progressive muscle weakness, which can make it harder to walk, climb stairs, or perform everyday tasks. At the same time, the heart muscle becomes stretched and weakened, a condition known as dilated cardiomyopathy. When the heart is dilated, it cannot pump blood as efficiently as it should, which can lead to heart failure symptoms such as shortness of breath, fatigue, and swelling in the legs or feet. This condition typically

Which specialists treat Neuromuscular disease with dilated cardiomyopathy?

2 specialists and care centers treating Neuromuscular disease with dilated cardiomyopathy are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.