Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome

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ORPHA:453499OMIM:616580Q87.8
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Overview

Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome is an extremely rare genetic condition that affects multiple body systems at the same time. The name describes its main features: problems with brain development (neurodevelopmental disorder), unusual facial features (craniofacial dysmorphism), heart defects (cardiac defect), and bone or skeletal problems (skeletal anomalies). Children born with this syndrome typically show developmental delays, meaning they may be slower to reach milestones like sitting, walking, and talking. Intellectual disability can range from mild to severe. Facial features may include a broad forehead, widely spaced eyes, a flat nasal bridge, or other distinctive characteristics. Heart defects can vary in type and severity, and some may require surgical correction. Skeletal problems might include abnormalities of the spine, fingers, toes, or limbs. Because this syndrome affects so many different parts of the body, care usually involves a team of specialists working together. Treatment is mainly supportive and focused on managing individual symptoms, such as surgery for heart defects, physical therapy for motor delays, speech therapy, and special education services. There is currently no cure, but early intervention can significantly improve quality of life. This condition is caused by mutations in the WAC gene and follows an autosomal dominant inheritance pattern, meaning only one copy of the altered gene is needed to cause the condition.

Also known as:

Key symptoms:

Developmental delays in walking and talkingIntellectual disabilityUnusual facial featuresHeart defects present at birthSkeletal abnormalities such as curved spine or finger differencesLow muscle tone (feeling floppy)Short stature or growth delaysFeeding difficulties in infancySpeech and language delaysBehavioral challengesWidely spaced eyesBroad or prominent foreheadSeizures in some casesJoint looseness or hypermobility

Clinical phenotype terms (50)— hover any for plain English
Abnormal helix morphologyHP:0011039Furrowed tongueHP:0000221
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome.

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No actively recruiting trials found for Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome at this time.

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No specialists are currently listed for Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific symptoms should I watch for as my child grows?,Does my child have a heart defect, and if so, what treatment is needed?,What therapies should we start right away to support development?,How often should my child have follow-up appointments with each specialist?,Should other family members be tested for the WAC gene change?,Are there any clinical trials or research studies my child could participate in?,What educational supports and services should I request for my child at school?

Common questions about Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome

What is Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome?

Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome is an extremely rare genetic condition that affects multiple body systems at the same time. The name describes its main features: problems with brain development (neurodevelopmental disorder), unusual facial features (craniofacial dysmorphism), heart defects (cardiac defect), and bone or skeletal problems (skeletal anomalies). Children born with this syndrome typically show developmental delays, meaning they may be slower to reach milestones like sitting, walking, and talking. Intellectual disabilit

How is Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome inherited?

Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome typically begin?

Typical onset of Neurodevelopmental disorder-craniofacial dysmorphism-cardiac defect-skeletal anomalies syndrome is neonatal. Age of onset can vary across affected individuals.