Myopathy with hexagonally cross-linked tubular arrays

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Overview

Myopathy with hexagonally cross-linked tubular arrays is an extremely rare inherited muscle disease. The name comes from a distinctive pattern seen when muscle tissue is examined under an electron microscope — tiny tube-like structures arranged in a hexagonal (six-sided) pattern are found within the muscle fibers. These abnormal structures are a hallmark of this condition and help doctors distinguish it from other muscle diseases. People with this condition typically experience muscle weakness that can affect various parts of the body. The weakness may involve the limbs, making it harder to walk, climb stairs, or lift objects. Some individuals also experience muscle stiffness, cramping, or exercise intolerance, meaning their muscles tire out more quickly than expected during physical activity. The severity of symptoms can vary from person to person, with some people having mild weakness and others experiencing more significant limitations. There is currently no cure for this condition. Treatment focuses on managing symptoms and maintaining function. Physical therapy, occupational therapy, and supportive care are the main approaches used to help patients stay as active and independent as possible. Because this disease is so rare, research is limited, and much remains to be learned about its full range of symptoms and long-term outlook.

Key symptoms:

Muscle weakness in the arms and legsExercise intolerance or easy muscle fatigueMuscle stiffnessMuscle crampsDifficulty walking or climbing stairsDifficulty lifting objects overheadReduced muscle bulk or muscle wastingGeneralized fatigueDifficulty with physical activities

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Myopathy with hexagonally cross-linked tubular arrays.

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No actively recruiting trials found for Myopathy with hexagonally cross-linked tubular arrays at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Myopathy with hexagonally cross-linked tubular arrays community →

No specialists are currently listed for Myopathy with hexagonally cross-linked tubular arrays.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Myopathy with hexagonally cross-linked tubular arrays.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Myopathy with hexagonally cross-linked tubular arrays

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my condition based on the biopsy and other test results?,Is genetic testing recommended for me and my family members?,What kind of physical therapy program would be most helpful?,Are there any activities I should avoid to protect my muscles?,How often should I have follow-up appointments to monitor my condition?,Are there any clinical trials or research studies I could participate in?,What signs or symptoms should prompt me to seek urgent medical attention?

Common questions about Myopathy with hexagonally cross-linked tubular arrays

What is Myopathy with hexagonally cross-linked tubular arrays?

Myopathy with hexagonally cross-linked tubular arrays is an extremely rare inherited muscle disease. The name comes from a distinctive pattern seen when muscle tissue is examined under an electron microscope — tiny tube-like structures arranged in a hexagonal (six-sided) pattern are found within the muscle fibers. These abnormal structures are a hallmark of this condition and help doctors distinguish it from other muscle diseases. People with this condition typically experience muscle weakness that can affect various parts of the body. The weakness may involve the limbs, making it harder to w