MMEP syndrome

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ORPHA:3434OMIM:601349Q87.8
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1Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

MMEP syndrome is an extremely rare genetic condition whose name stands for Microcephaly, Mesobrachyphalangy, and Tracheoesophageal fistula, though it is also sometimes referred to by its Orphanet designation (ORPHA:3434). This syndrome affects multiple body systems from birth. The hallmark features include an unusually small head size (microcephaly), shortened middle bones of the fingers (mesobrachyphalangy), and an abnormal connection between the windpipe and the food pipe (tracheoesophageal fistula). Additional features may include intellectual disability, growth delays, and other skeletal or limb abnormalities. Because MMEP syndrome is so rare, with only a handful of cases described in the medical literature, our understanding of the full range of symptoms and the best approaches to treatment remains limited. There is currently no cure for MMEP syndrome. Treatment is supportive and focuses on managing individual symptoms. For example, a tracheoesophageal fistula typically requires surgical repair shortly after birth to allow safe feeding and breathing. Developmental support, physical therapy, and regular monitoring by a team of specialists are important parts of ongoing care. Early diagnosis and coordinated multidisciplinary management can help improve quality of life for affected individuals.

Also known as:

Key symptoms:

Unusually small head size (microcephaly)Shortened middle finger bonesAbnormal connection between the windpipe and food pipe (tracheoesophageal fistula)Intellectual disabilityGrowth delaysFeeding difficulties in infancyBreathing problemsLimb or skeletal abnormalitiesDevelopmental delays

Clinical phenotype terms (11)— hover any for plain English
Split footHP:0001839
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for MMEP syndrome.

View clinical trials →

No actively recruiting trials found for MMEP syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the MMEP syndrome community →

Specialists

1 foundView all specialists →
MM
Martin Hardmeier, PD Dr. med
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to MMEP syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about MMEP syndrome

No recent news articles for MMEP syndrome.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the severity of my child's tracheoesophageal fistula, and when should surgery be performed?,What developmental therapies should we start, and how often?,Should we pursue genetic testing such as whole exome sequencing to look for a specific cause?,What are the long-term expectations for my child's growth and development?,Are there any other specialists we should see regularly?,What signs or symptoms should prompt us to seek emergency care?,Are there any research studies or registries we can participate in?

Common questions about MMEP syndrome

What is MMEP syndrome?

MMEP syndrome is an extremely rare genetic condition whose name stands for Microcephaly, Mesobrachyphalangy, and Tracheoesophageal fistula, though it is also sometimes referred to by its Orphanet designation (ORPHA:3434). This syndrome affects multiple body systems from birth. The hallmark features include an unusually small head size (microcephaly), shortened middle bones of the fingers (mesobrachyphalangy), and an abnormal connection between the windpipe and the food pipe (tracheoesophageal fistula). Additional features may include intellectual disability, growth delays, and other skeletal o

At what age does MMEP syndrome typically begin?

Typical onset of MMEP syndrome is neonatal. Age of onset can vary across affected individuals.

Which specialists treat MMEP syndrome?

1 specialists and care centers treating MMEP syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.