Microcephaly-complex motor and sensory axonal neuropathy syndrome

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Overview

Microcephaly-complex motor and sensory axonal neuropathy syndrome is a very rare inherited neurological condition that affects the brain and the nerves throughout the body. 'Microcephaly' means that the head and brain are smaller than usual, which can affect thinking, learning, and development. The 'axonal neuropathy' part means that the long fibers of nerve cells — called axons — that carry signals between the brain, spinal cord, muscles, and skin are damaged. This affects both movement (motor nerves) and sensation (sensory nerves). People with this condition typically show signs from birth or very early in life. Common features include a small head size, delayed development, intellectual disability, muscle weakness, difficulty walking, and reduced ability to feel touch, pain, or temperature in the hands and feet. The combination of brain underdevelopment and nerve damage makes this a complex, multi-system neurological disorder. There is currently no cure for this syndrome. Care focuses on managing symptoms, supporting development, and improving quality of life through physical therapy, occupational therapy, and educational support. Because this condition is so rare, treatment is highly individualized and managed by a team of specialists.

Key symptoms:

Smaller than normal head size (microcephaly)Intellectual disability or learning difficultiesDelayed developmental milestones such as sitting, standing, or walkingMuscle weakness, especially in the arms and legsReduced or absent reflexesDifficulty walking or unsteady gaitNumbness or reduced sensation in the hands and feetMuscle wasting (loss of muscle bulk over time)Foot deformities such as high arches or curled toesDifficulty with fine motor tasks like writing or buttoning clothesSpeech and language delays

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Microcephaly-complex motor and sensory axonal neuropathy syndrome.

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No actively recruiting trials found for Microcephaly-complex motor and sensory axonal neuropathy syndrome at this time.

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No specialists are currently listed for Microcephaly-complex motor and sensory axonal neuropathy syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Microcephaly-complex motor and sensory axonal neuropathy syndrome.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which gene is causing this condition in my child, and what does that mean for other family members?,What therapies should we start right away, and how often should they happen?,Are there any clinical trials or research studies we could participate in?,What signs should prompt us to seek emergency care?,How is this condition likely to progress over time, and what should we expect as my child gets older?,Should other family members be tested for the gene change?,What educational and community support resources are available for our family?

Common questions about Microcephaly-complex motor and sensory axonal neuropathy syndrome

What is Microcephaly-complex motor and sensory axonal neuropathy syndrome?

Microcephaly-complex motor and sensory axonal neuropathy syndrome is a very rare inherited neurological condition that affects the brain and the nerves throughout the body. 'Microcephaly' means that the head and brain are smaller than usual, which can affect thinking, learning, and development. The 'axonal neuropathy' part means that the long fibers of nerve cells — called axons — that carry signals between the brain, spinal cord, muscles, and skin are damaged. This affects both movement (motor nerves) and sensation (sensory nerves). People with this condition typically show signs from birth

How is Microcephaly-complex motor and sensory axonal neuropathy syndrome inherited?

Microcephaly-complex motor and sensory axonal neuropathy syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Microcephaly-complex motor and sensory axonal neuropathy syndrome typically begin?

Typical onset of Microcephaly-complex motor and sensory axonal neuropathy syndrome is neonatal. Age of onset can vary across affected individuals.