Microcephaly-cervical spine fusion anomalies syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:2522OMIM:251250Q87.8
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Microcephaly-cervical spine fusion anomalies syndrome is an extremely rare genetic condition that combines an unusually small head (microcephaly) with abnormal fusion of the bones in the neck (cervical vertebrae). This syndrome is sometimes also referred to as microcephaly with cervical spine fusion or may overlap with descriptions of Klippel-Feil-like anomalies combined with microcephaly. Children born with this condition typically have a noticeably smaller head circumference than expected for their age, which often reflects reduced brain growth. The fused neck bones can limit the range of motion in the neck and may cause a short neck appearance. Beyond the two main features, affected individuals may also have intellectual disability of varying degrees, short stature, and other skeletal abnormalities. Some patients may have facial differences and neurological problems related to the small brain size. Because this syndrome is so rare, the full range of symptoms is not completely understood, and new features may be recognized as more cases are described. There is currently no cure for this condition. Treatment focuses on managing symptoms and supporting development. This may include physical therapy, occupational therapy, special education services, and orthopedic care for spinal issues. Regular monitoring by multiple specialists is important to address complications as they arise and to optimize quality of life.

Key symptoms:

Unusually small head size (microcephaly)Fused bones in the neck (cervical spine fusion)Limited neck movementShort neckIntellectual disabilityDevelopmental delaysShort statureLow hairline at the back of the headFacial differencesNeurological problemsPossible hearing difficultiesSkeletal abnormalities beyond the neck

Clinical phenotype terms (26)— hover any for plain English
Spinal cord compressionHP:0002176Fused cervical vertebraeHP:0002949
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Microcephaly-cervical spine fusion anomalies syndrome.

View clinical trials →

No actively recruiting trials found for Microcephaly-cervical spine fusion anomalies syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Microcephaly-cervical spine fusion anomalies syndrome community →

No specialists are currently listed for Microcephaly-cervical spine fusion anomalies syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Microcephaly-cervical spine fusion anomalies syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Microcephaly-cervical spine fusion anomalies syndromeForum →

No community posts yet. Be the first to share your experience with Microcephaly-cervical spine fusion anomalies syndrome.

Start the conversation →

Latest news about Microcephaly-cervical spine fusion anomalies syndrome

No recent news articles for Microcephaly-cervical spine fusion anomalies syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my child's microcephaly, and what does this mean for their development?,Which cervical vertebrae are fused, and is there any risk to the spinal cord?,Are there any activities or movements we should avoid to protect the neck?,What therapies do you recommend, and how often should they occur?,Should we pursue genetic testing, and what might the results tell us?,How often should imaging of the spine be repeated?,Are there any clinical studies or research programs we could participate in?

Common questions about Microcephaly-cervical spine fusion anomalies syndrome

What is Microcephaly-cervical spine fusion anomalies syndrome?

Microcephaly-cervical spine fusion anomalies syndrome is an extremely rare genetic condition that combines an unusually small head (microcephaly) with abnormal fusion of the bones in the neck (cervical vertebrae). This syndrome is sometimes also referred to as microcephaly with cervical spine fusion or may overlap with descriptions of Klippel-Feil-like anomalies combined with microcephaly. Children born with this condition typically have a noticeably smaller head circumference than expected for their age, which often reflects reduced brain growth. The fused neck bones can limit the range of mo

How is Microcephaly-cervical spine fusion anomalies syndrome inherited?

Microcephaly-cervical spine fusion anomalies syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Microcephaly-cervical spine fusion anomalies syndrome typically begin?

Typical onset of Microcephaly-cervical spine fusion anomalies syndrome is neonatal. Age of onset can vary across affected individuals.