Metaphyseal chondrodysplasia, Kaitila type

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ORPHA:166038OMIM:250230Q78.5
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Overview

Metaphyseal chondrodysplasia, Kaitila type is an extremely rare inherited bone disorder that affects how bones grow, particularly at the metaphyses — the wide portions near the ends of long bones. This condition is also sometimes referred to as metaphyseal dysplasia, Kaitila type. It belongs to a group of skeletal disorders called metaphyseal chondrodysplasias, where the cartilage-to-bone conversion process at the growth plates does not work properly. People with this condition typically show short stature and skeletal abnormalities that become apparent during childhood. The metaphyses of the long bones appear widened and irregular on X-rays. Affected individuals may have bowed legs, waddling gait, and joint problems. The severity can vary, but the condition primarily impacts the skeletal system. Because this is such a rare condition, there is no specific cure or targeted therapy available. Treatment is mainly supportive and focuses on managing symptoms. This may include orthopedic interventions for bone deformities, physical therapy to maintain mobility, and regular monitoring of growth and skeletal development. Pain management may also be necessary. Genetic counseling is recommended for affected families to understand the inheritance pattern and recurrence risk.

Key symptoms:

Short statureBowed legsWidened ends of long bonesWaddling gaitJoint stiffness or limited range of motionIrregular growth plates visible on X-rayMild to moderate limb shorteningBone painDifficulty with physical activities

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Metaphyseal chondrodysplasia, Kaitila type.

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No actively recruiting trials found for Metaphyseal chondrodysplasia, Kaitila type at this time.

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No specialists are currently listed for Metaphyseal chondrodysplasia, Kaitila type.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Metaphyseal chondrodysplasia, Kaitila type.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my child's skeletal involvement based on current X-rays?,Will my child need surgery to correct bone deformities?,What is the expected adult height for my child?,Should we pursue genetic testing to confirm the diagnosis?,What physical activities are safe, and which should be avoided?,How often should we schedule follow-up X-rays and orthopedic visits?,Are there any clinical trials or research studies we could participate in?

Common questions about Metaphyseal chondrodysplasia, Kaitila type

What is Metaphyseal chondrodysplasia, Kaitila type?

Metaphyseal chondrodysplasia, Kaitila type is an extremely rare inherited bone disorder that affects how bones grow, particularly at the metaphyses — the wide portions near the ends of long bones. This condition is also sometimes referred to as metaphyseal dysplasia, Kaitila type. It belongs to a group of skeletal disorders called metaphyseal chondrodysplasias, where the cartilage-to-bone conversion process at the growth plates does not work properly. People with this condition typically show short stature and skeletal abnormalities that become apparent during childhood. The metaphyses of the

How is Metaphyseal chondrodysplasia, Kaitila type inherited?

Metaphyseal chondrodysplasia, Kaitila type follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Metaphyseal chondrodysplasia, Kaitila type typically begin?

Typical onset of Metaphyseal chondrodysplasia, Kaitila type is childhood. Age of onset can vary across affected individuals.