Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13)

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Overview

Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) is a very rare and aggressive type of blood cancer that mainly affects infants and very young children. It is also known as AMKL with t(1;22) or acute megakaryoblastic leukemia with the RBM15-MRTFA fusion. In this disease, the bone marrow produces abnormal blood cells called megakaryoblasts, which are immature cells that would normally develop into the platelets that help your blood clot. Because of a specific genetic change — a swap of material between chromosomes 1 and 22 — these cells grow out of control and crowd out healthy blood cells. Children with this condition often show signs such as low blood counts, easy bruising or bleeding, fatigue, pale skin, fevers, and an enlarged liver or spleen. Some infants may also develop areas of abnormal tissue growth outside the bone marrow. The disease is almost exclusively seen in babies and children under the age of three, and it is not inherited from parents — the chromosome change happens on its own during early development. Treatment typically involves intensive chemotherapy designed for acute myeloid leukemia (AML). In some cases, a bone marrow (stem cell) transplant may be recommended. While this is a serious cancer, outcomes for infants with this specific chromosome change may be somewhat better compared to other forms of megakaryoblastic leukemia, especially when treated with modern intensive chemotherapy protocols. Ongoing research continues to explore targeted therapies and improved treatment strategies.

Also known as:

Key symptoms:

Extreme tiredness and fatiguePale skinEasy bruisingUnusual or excessive bleedingFrequent fevers or infectionsEnlarged liverEnlarged spleenSwollen belly in infantsPoor feeding or failure to thriveBone pain or irritabilityLow platelet countsLow red blood cell counts (anemia)Abnormal lumps or masses outside the bone marrow

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13).

View clinical trials →

No actively recruiting trials found for Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) community →

No specialists are currently listed for Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13).

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13).

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13)

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What is the specific treatment plan for my child, and how long will treatment last?,Is my child eligible for any clinical trials that might offer newer or targeted treatments?,What are the short-term and long-term side effects of the chemotherapy my child will receive?,Will my child need a bone marrow transplant, and if so, how do we find a donor?,What signs of complications should I watch for at home, and when should I go to the emergency room?,How will this treatment affect my child's growth and development in the long term?,What support services are available for our family during and after treatment?

Common questions about Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13)

What is Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13)?

Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) is a very rare and aggressive type of blood cancer that mainly affects infants and very young children. It is also known as AMKL with t(1;22) or acute megakaryoblastic leukemia with the RBM15-MRTFA fusion. In this disease, the bone marrow produces abnormal blood cells called megakaryoblasts, which are immature cells that would normally develop into the platelets that help your blood clot. Because of a specific genetic change — a swap of material between chromosomes 1 and 22 — these cells grow out of control and crowd out healthy blo

How is Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) inherited?

Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) typically begin?

Typical onset of Megakaryoblastic acute myeloid leukemia with t(1;22)(p13;q13) is infantile. Age of onset can vary across affected individuals.