Marie Unna hereditary hypotrichosis

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ORPHA:444OMIM:146550Q84.0
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Overview

Marie Unna hereditary hypotrichosis (MUHH) is a rare inherited condition that affects hair growth. It is also sometimes called Marie Unna hypotrichosis or hereditary hypotrichosis Marie Unna type. The condition causes unusual hair patterns that change over a person's lifetime in a very specific way. Babies are often born with little or no hair, or sometimes with coarse, wiry hair that looks unusual. During early childhood, hair may actually grow back and appear somewhat normal, but then — usually during or after puberty — hair loss begins again and becomes permanent. This second phase of hair loss tends to affect the scalp, eyebrows, eyelashes, and body hair. The hair loss in MUHH is not caused by inflammation or scarring in the way some other hair loss conditions are, though over time the hair follicles can become permanently damaged. The condition does not affect intelligence, organ function, or overall health — it is primarily a cosmetic and emotional concern. There is no cure at this time, and treatment focuses on managing the appearance of hair loss. Options include wigs, hairpieces, and cosmetic approaches. Because the condition is rare and mainly affects appearance, research into targeted therapies is limited, but genetic testing can confirm the diagnosis and help families understand the risk of passing it on to children.

Also known as:

Key symptoms:

Little or no hair at birth, or coarse and wiry hair in infancyTemporary improvement in hair growth during early childhoodProgressive hair loss starting around pubertyThinning or complete loss of scalp hair in adulthoodLoss or thinning of eyebrowsLoss or thinning of eyelashesReduced or absent body hairCoarse or twisted hair texture when hair is presentHair that breaks easily or grows slowlyPermanent hair follicle damage over time

Clinical phenotype terms (5)— hover any for plain English
Sparse or absent eyelashesHP:0200102
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Marie Unna hereditary hypotrichosis.

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No actively recruiting trials found for Marie Unna hereditary hypotrichosis at this time.

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No specialists are currently listed for Marie Unna hereditary hypotrichosis.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

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Caregiver Resources

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.Can genetic testing confirm the diagnosis for me and my family, and which genes should be tested?,What is the likely pattern of hair loss for my child or for me as the condition progresses?,Are there any treatments — even experimental ones — that might slow or reduce hair loss?,What cosmetic options do you recommend, and can any of these be covered by insurance?,Should other family members be tested, and what does this diagnosis mean for my children's risk?,Can you refer me to a psychologist or support group who has experience with hair loss conditions?,Are there any clinical trials or research studies I should know about?

Common questions about Marie Unna hereditary hypotrichosis

What is Marie Unna hereditary hypotrichosis?

Marie Unna hereditary hypotrichosis (MUHH) is a rare inherited condition that affects hair growth. It is also sometimes called Marie Unna hypotrichosis or hereditary hypotrichosis Marie Unna type. The condition causes unusual hair patterns that change over a person's lifetime in a very specific way. Babies are often born with little or no hair, or sometimes with coarse, wiry hair that looks unusual. During early childhood, hair may actually grow back and appear somewhat normal, but then — usually during or after puberty — hair loss begins again and becomes permanent. This second phase of hair

How is Marie Unna hereditary hypotrichosis inherited?

Marie Unna hereditary hypotrichosis follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Marie Unna hereditary hypotrichosis typically begin?

Typical onset of Marie Unna hereditary hypotrichosis is neonatal. Age of onset can vary across affected individuals.