Male infertility due to NANOS1 mutation

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Overview

Male infertility due to NANOS1 mutation is a rare genetic condition in which changes (mutations) in the NANOS1 gene lead to problems with sperm production, resulting in the inability to father children naturally. The NANOS1 gene plays an important role in the development and survival of germ cells, which are the cells that eventually become sperm. When this gene does not work properly, the testes may produce very few sperm (severe oligozoospermia) or no sperm at all (azoospermia). Men with this condition typically have normal physical development, normal hormone levels, and no other health problems — the only sign is difficulty conceiving a child. This condition is usually discovered in adulthood when a man and his partner seek medical help for infertility. A semen analysis will show very low or absent sperm counts. Because the condition is genetic, it does not respond to hormonal treatments or lifestyle changes aimed at improving sperm production. However, in some cases where a small number of sperm are still produced, assisted reproductive technologies such as intracytoplasmic sperm injection (ICSI) combined with in vitro fertilization (IVF) may offer a chance at biological parenthood. Genetic counseling is recommended for affected individuals and their families to understand the inheritance pattern and implications for future generations.

Key symptoms:

Inability to conceive a child naturallyVery low sperm count (oligozoospermia)Absence of sperm in semen (azoospermia)Normal physical and sexual developmentNormal testosterone levelsNormal-sized testes in some casesReduced testicular volume in some cases

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Male infertility due to NANOS1 mutation.

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No actively recruiting trials found for Male infertility due to NANOS1 mutation at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Male infertility due to NANOS1 mutation community →

No specialists are currently listed for Male infertility due to NANOS1 mutation.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is there any chance that sperm can be found in my testes even if my semen analysis shows no sperm?,Would a surgical sperm retrieval procedure like micro-TESE be an option for me?,What are our chances of success with IVF and ICSI given my specific situation?,If we use assisted reproduction, could this mutation be passed on to our sons?,Should my family members be tested for this mutation?,Are there any clinical trials or new research for this type of genetic infertility?,Can you recommend a genetic counselor who specializes in reproductive genetics?

Common questions about Male infertility due to NANOS1 mutation

What is Male infertility due to NANOS1 mutation?

Male infertility due to NANOS1 mutation is a rare genetic condition in which changes (mutations) in the NANOS1 gene lead to problems with sperm production, resulting in the inability to father children naturally. The NANOS1 gene plays an important role in the development and survival of germ cells, which are the cells that eventually become sperm. When this gene does not work properly, the testes may produce very few sperm (severe oligozoospermia) or no sperm at all (azoospermia). Men with this condition typically have normal physical development, normal hormone levels, and no other health pro

How is Male infertility due to NANOS1 mutation inherited?

Male infertility due to NANOS1 mutation follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Male infertility due to NANOS1 mutation typically begin?

Typical onset of Male infertility due to NANOS1 mutation is adult. Age of onset can vary across affected individuals.