Lipodystrophy due to peptidic growth factors deficiency

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ORPHA:1979OMIM:233805E88.1
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2Active trials8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Lipodystrophy due to peptidic growth factors deficiency is an extremely rare condition that belongs to a group of disorders called lipodystrophies, which are characterized by abnormal loss or absence of body fat (adipose tissue). In this specific form, the loss of fat tissue is linked to a deficiency in certain peptide growth factors — small proteins that normally help fat cells grow, survive, and function properly. Without adequate levels of these growth factors, the body cannot maintain normal fat stores. People with this condition may notice a partial or generalized loss of fat under the skin, which can change their physical appearance. Because fat tissue plays an important role in metabolism, the loss of fat can lead to serious metabolic problems including insulin resistance, diabetes, high levels of triglycerides (fats) in the blood, and fatty liver disease. These metabolic complications can affect the heart, liver, and other organs over time. Because this condition is so rare, treatment is largely supportive and focused on managing the metabolic complications. This may include dietary modifications, medications to control blood sugar and lipid levels, and in some cases, leptin replacement therapy if leptin deficiency is present. Close monitoring by a team of specialists is important to prevent long-term organ damage.

Also known as:

Key symptoms:

Loss of body fat under the skinVisible lack of fat in the face, arms, legs, or trunkProminent muscles and veins due to fat lossInsulin resistance or diabetesHigh triglyceride levels in the bloodEnlarged liver or fatty liver diseaseIncreased appetiteDark, velvety skin patches (acanthosis nigricans)Irregular menstrual periods in womenFatigueDifficulty gaining or maintaining weightJoint or muscle pain

Clinical phenotype terms (28)— hover any for plain English
Reduced subcutaneous adipose tissueHP:0003758LipodystrophyHP:0009125Lack of skin elasticityHP:0100679
Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗OMIM ↗NORD ↗

FDA & Trial Timeline

2 events
Sep 2025Tirzepatide for Partial Lipodystrophy Treatment: A New Horizon in 2024

University of Michigan — PHASE2

TrialRECRUITING
Oct 2016MEASuRE: Metreleptin Effectiveness And Safety Registry

Amryt Pharma

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Lipodystrophy due to peptidic growth factors deficiency.

2 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

2 recruitingView all trials with filters →
Phase 21 trial
Tirzepatide for Partial Lipodystrophy Treatment: A New Horizon in 2024
Phase 2
Actively Recruiting
PI: Elif Oral, MD (University of Michigan) · Sites: Ann Arbor, Michigan · Age: 1899 yrs
Other1 trial
MEASuRE: Metreleptin Effectiveness And Safety Registry
Actively Recruiting
PI: Lori Hartnett (Amryt Pharmaceuticals DAC) · Sites: Birmingham, Alabama; Duarte, California +26 more

No specialists are currently listed for Lipodystrophy due to peptidic growth factors deficiency.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Lipodystrophy due to peptidic growth factors deficiency.

Search all travel grants →NORD Financial Assistance ↗

Community

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Caregiver Resources

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Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific growth factors are deficient in my case, and how were they measured?,Am I a candidate for leptin replacement therapy (metreleptin)?,How often should my blood sugar, triglycerides, and liver function be monitored?,What dietary plan do you recommend to manage my metabolic complications?,Are there any clinical trials or research studies I could participate in?,What signs or symptoms should prompt me to seek emergency care?,Should my family members be tested for this condition?

Common questions about Lipodystrophy due to peptidic growth factors deficiency

What is Lipodystrophy due to peptidic growth factors deficiency?

Lipodystrophy due to peptidic growth factors deficiency is an extremely rare condition that belongs to a group of disorders called lipodystrophies, which are characterized by abnormal loss or absence of body fat (adipose tissue). In this specific form, the loss of fat tissue is linked to a deficiency in certain peptide growth factors — small proteins that normally help fat cells grow, survive, and function properly. Without adequate levels of these growth factors, the body cannot maintain normal fat stores. People with this condition may notice a partial or generalized loss of fat under the s

Are there clinical trials for Lipodystrophy due to peptidic growth factors deficiency?

Yes — 2 recruiting clinical trials are currently listed for Lipodystrophy due to peptidic growth factors deficiency on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.