Leukodystrophy

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ORPHA:68356
Who is this for?
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8Active trials35Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Leukodystrophy is not a single disease but a group of rare, progressive disorders that affect the white matter of the brain and spinal cord. White matter is made up of nerve fibers covered by a protective coating called myelin, which helps nerve signals travel quickly and efficiently. In leukodystrophies, myelin is either not made properly, breaks down over time, or is not maintained correctly. This disrupts communication between different parts of the brain and the rest of the body. Because there are many different types of leukodystrophy — each caused by a different genetic change — symptoms can vary widely from person to person. Common problems include difficulty walking, muscle stiffness or weakness, trouble with speech and swallowing, vision or hearing loss, seizures, and a decline in thinking and learning abilities. Some forms appear in infancy or early childhood, while others may not show up until adulthood. Treatment depends on the specific type of leukodystrophy. Some forms have targeted therapies, such as hematopoietic stem cell transplantation (bone marrow transplant) for certain types like adrenoleukodystrophy, or enzyme replacement therapy for others. However, many types currently have no cure, and care focuses on managing symptoms and improving quality of life. Research is actively ongoing, with gene therapy showing promise for several forms.

Key symptoms:

Difficulty walking or loss of ability to walkMuscle stiffness or spasticityMuscle weaknessProblems with balance and coordinationSlurred or lost speechDifficulty swallowingVision loss or abnormal eye movementsHearing lossSeizuresDecline in memory, thinking, or learningBehavioral or personality changesLoss of previously learned skills (developmental regression)Fatigue and low energyBladder or bowel control problemsAdrenal gland problems (in some types like ALD)

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

8 events
Sep 2025An Open-label, Single Center, Single Participant Study of an Experimental Antisense Oligonucleotide Treatment for TUBB4A-related Leukodystrophy

University of California, San Diego — PHASE1, PHASE2

TrialACTIVE NOT RECRUITING
Sep 2024Single Participant Study of an Experimental ASO Treatment for TUBB4A-related Leukodystrophy

Massachusetts General Hospital — PHASE1, PHASE2

TrialENROLLING BY INVITATION
Mar 2024A Study of Participants With Cerebral Adrenoleukodystrophy (CALD) Treated With Elivaldogene Autotemcel

Genetix Biotherapeutics Inc. — NA

TrialRECRUITING
Jul 2023A Clinical Study to Assess the Efficacy and Safety of Leriglitazone in Adult Male Subjects With Cerebral Adrenoleukodystrophy

Minoryx Therapeutics, S.L. — PHASE3

TrialRECRUITING
Mar 2023An Open-Label Exploratory Study of Fosigotifator in Participants With Vanishing White Matter Disease

Calico Life Sciences LLC — PHASE1, PHASE2

TrialRECRUITING
Dec 2016The Myelin Disorders Biorepository Project

Children's Hospital of Philadelphia — NA

TrialRECRUITING
Sep 2014UCB Transplant of Inherited Metabolic Diseases With Administration of Intrathecal UCB Derived Oligodendrocyte-Like Cells

Joanne Kurtzberg, MD — PHASE1

TrialRECRUITING
Jan 2007Natural History, Diagnosis, and Outcomes for Leukodystrophies

University of Utah

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Leukodystrophy.

8 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

8 recruitingView all trials with filters →
Phase 31 trial
A Clinical Study to Assess the Efficacy and Safety of Leriglitazone in Adult Male Subjects With Cerebral Adrenoleukodystrophy
Phase 3
Actively Recruiting
· Sites: Palo Alto, California; Gainesville, Florida +11 more · Age: 1899 yrs
Phase 11 trial
UCB Transplant of Inherited Metabolic Diseases With Administration of Intrathecal UCB Derived Oligodendrocyte-Like Cells
Phase 1
Actively Recruiting
PI: Joanne Kurtzberg, MD (Duke University) · Sites: Durham, North Carolina · Age: 022 yrs
N/A2 trials
A Study of Participants With Cerebral Adrenoleukodystrophy (CALD) Treated With Elivaldogene Autotemcel
N/A
Actively Recruiting
PI: Kiran Bhirangi, MD (bluebird bio, Inc.) · Sites: Boston, Massachusetts; Philadelphia, Pennsylvania +1 more
The Myelin Disorders Biorepository Project
N/A
Actively Recruiting
PI: Adeline Vanderver, MD (Children's Hospital of Philadelphia) · Sites: Los Angeles, California; Orange, California +18 more
Other1 trial
Natural History, Diagnosis, and Outcomes for Leukodystrophies
Actively Recruiting
· Sites: Salt Lake City, Utah

Specialists

Showing 25 of 35View all specialists →
PM
Patrick Aubourg, MD-PhD
Specialist
PI on 1 active trial
TP
Thomas Roujeau, MD, PhD
Specialist
PI on 1 active trial
CM
Caroline Sevin, MD-PhD
Specialist
PI on 1 active trial
NP
Nathalie Cartier, MD, PhD
Specialist
PI on 1 active trial
RM
Raphael Schiffmann, MD, MHS
DALLAS, TX
Specialist
PI on 1 active trial
VC
Valeria Calbi
Specialist
4 Leukodystrophy publications
LL
Lucia Laugwitz
Specialist
4 Leukodystrophy publications
SG
Samuel Groeschel
Specialist
3 Leukodystrophy publications
AZ
Ayelet Zerem
Specialist
3 Leukodystrophy publications
NW
Nicole I Wolf
Specialist
3 Leukodystrophy publications
CB
Cristina Baldoli
Specialist
3 Leukodystrophy publications
GB
Geneviève Bernard
Specialist
3 Leukodystrophy publications
CB
Caroline Bergner
Specialist
2 Leukodystrophy publications
DS
Daphne H Schoenmakers
Specialist
2 Leukodystrophy publications
JB
Jaap Jan Boelens
NEW YORK, NY
Specialist
2 Leukodystrophy publications
DR
Dipak Ram
Specialist
2 Leukodystrophy publications
FM
Fanny Mochel
Specialist
2 Leukodystrophy publications
FF
Francesca Fumagalli
Specialist
6 Leukodystrophy publications
PM
Paul Orchard, MD
MINNEAPOLIS, MN
Specialist
PI on 15 active trials
FM
Florian Eichler, MD
BOSTON, MA
Specialist
PI on 4 active trials
MM
Maria L Escolar, MD
CHAPEL HILL, NC
Specialist
PI on 1 active trial
WM
William A Gahl, M.D.
Bethesda, Maryland
Specialist

Rare Disease Specialist

PI on 12 active trials
TM
Thomas J. Langan, MD
Specialist
PI on 1 active trial
MM
Mitchell S Cairo, MD
HAWTHORNE, NY
Specialist
PI on 12 active trials
AM
Adeline Vanderver, MD
Los Angeles, California
Specialist

Rare Disease Specialist

PI on 4 active trials1 Leukodystrophy publication

Treatment Centers

8 centers
⚗️ Trial Site

Children's Hospital of Orange County

📍 Orange, California

👤 Richard Neibeger, MD

⚗️ Trial Site

Children's National Medical Center

📍 Washington D.C., District of Columbia

👤 Richard Neibeger, MD

⚗️ Trial Site

Ann & Robert H. Lurie Children's Hospital of Chicago

📍 Chicago, Illinois

⚗️ Trial Site

Nationwide Children's Hospital

📍 Columbus, Ohio

⚗️ Trial Site

University of Minnesota

📍 Minneapolis, Minnesota

⚗️ Trial Site

University of Pittsburgh Medical Center

📍 Pittsburgh, Pennsylvania

⚗️ Trial Site

Mayo Clinic

📍 Jacksonville, Florida

⚗️ Trial Site

University of Pennsylvania

📍 Philadelphia, Pennsylvania

Travel Grants

No travel grants are currently matched to Leukodystrophy.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Leukodystrophy

Disease timeline:

New recruiting trial: Natural History, Diagnosis, and Outcomes for Leukodystrophies

A new clinical trial is recruiting patients for Leukodystrophy

New trial: The Myelin Disorders Biorepository Project

Phase NA trial recruiting.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which specific type of leukodystrophy has been identified, and what does that mean for my child's or my own prognosis?,Is there an approved or experimental treatment available for this specific type, and are we eligible?,Should other family members be tested, and what are the chances of passing this on to future children?,What specialists should be part of our care team, and how often should we be seen?,Are there clinical trials we should consider, and how do we find out about new research?,What early warning signs should prompt us to seek emergency care?,What support services — such as therapy, school accommodations, or home care — are available to us?

Common questions about Leukodystrophy

What is Leukodystrophy?

Leukodystrophy is not a single disease but a group of rare, progressive disorders that affect the white matter of the brain and spinal cord. White matter is made up of nerve fibers covered by a protective coating called myelin, which helps nerve signals travel quickly and efficiently. In leukodystrophies, myelin is either not made properly, breaks down over time, or is not maintained correctly. This disrupts communication between different parts of the brain and the rest of the body. Because there are many different types of leukodystrophy — each caused by a different genetic change — symptom

Are there clinical trials for Leukodystrophy?

Yes — 8 recruiting clinical trials are currently listed for Leukodystrophy on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Leukodystrophy?

25 specialists and care centers treating Leukodystrophy are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.