Juvenile temporal arteritis

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Overview

Juvenile temporal arteritis is a rare condition where the walls of the temporal arteries — the blood vessels that run along the sides of your head near your temples — become inflamed. Unlike the more common form of temporal arteritis seen in older adults (called giant cell arteritis), this condition affects children, teenagers, and young adults, typically under the age of 40. It is sometimes called juvenile temporal arteritis or non-giant-cell temporal arteritis of the young. The inflammation causes the artery wall to thicken, which can be felt as a firm, painless or mildly tender lump or nodule near the temple. The condition does not usually cause the severe headaches, vision problems, or jaw pain that are common in the adult form. In most reported cases, the disease appears to be limited to the skin and the outer layer of the temporal artery, without spreading to other blood vessels or organs. Treatment usually involves surgical removal of the affected section of the artery, which is often both diagnostic and curative. Steroids and anti-inflammatory medications may also be used. The overall outlook for most patients is good, especially when the condition is caught and treated early.

Also known as:

Key symptoms:

A firm, painless or mildly tender lump near the templeSwelling or thickening of the temporal artery on one or both sides of the headVisible or palpable nodule under the skin near the templeMild local tenderness when touching the temple areaRedness or warmth over the affected area in some casesNo fever or systemic illness in most casesNo vision changes (unlike adult temporal arteritis)

Clinical phenotype terms (8)— hover any for plain English
Allergic rhinitisHP:0003193Cerebral ischemiaHP:0002637
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Juvenile

Begins in the teen years

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Juvenile temporal arteritis.

View clinical trials →

No actively recruiting trials found for Juvenile temporal arteritis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Juvenile temporal arteritis community →

No specialists are currently listed for Juvenile temporal arteritis.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Juvenile temporal arteritis.

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Community

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Latest news about Juvenile temporal arteritis

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Caregiver Resources

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Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is surgery the best option for my child, and what does the recovery look like?,Do we need to do any additional tests to rule out other types of vasculitis?,What are the chances this condition will come back after treatment?,Should my child see a rheumatologist for long-term follow-up?,Are there any signs or symptoms I should watch for that would mean we need to go to the emergency room?,Does my child need any blood tests or imaging scans after treatment?,Is there any known cause or risk factor that could affect other family members?

Common questions about Juvenile temporal arteritis

What is Juvenile temporal arteritis?

Juvenile temporal arteritis is a rare condition where the walls of the temporal arteries — the blood vessels that run along the sides of your head near your temples — become inflamed. Unlike the more common form of temporal arteritis seen in older adults (called giant cell arteritis), this condition affects children, teenagers, and young adults, typically under the age of 40. It is sometimes called juvenile temporal arteritis or non-giant-cell temporal arteritis of the young. The inflammation causes the artery wall to thicken, which can be felt as a firm, painless or mildly tender lump or nod

How is Juvenile temporal arteritis inherited?

Juvenile temporal arteritis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Juvenile temporal arteritis typically begin?

Typical onset of Juvenile temporal arteritis is juvenile. Age of onset can vary across affected individuals.