Jung syndrome

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ORPHA:2321OMIM:601427Q87.8
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Overview

Jung syndrome, also known as Jung-Bhatt-Bhatt syndrome or blepharophimosis with ptosis, syndactyly, and short stature, is an extremely rare genetic condition that affects multiple parts of the body. It was first described in the medical literature and is characterized by a combination of eye, hand, and growth abnormalities. People with Jung syndrome typically have narrow eye openings (blepharophimosis) and drooping eyelids (ptosis), which can affect vision and facial appearance. They may also have webbing or fusion of fingers or toes (syndactyly) and shorter-than-expected height (short stature). Additional features can include other skeletal differences and mild developmental concerns. Because this condition is so rare, with only a handful of cases reported in the medical literature, our understanding of the full range of symptoms and the best approaches to treatment is still limited. Treatment is mainly supportive and focused on managing individual symptoms, such as surgery for eyelid or hand abnormalities. A team of specialists is usually needed to provide comprehensive care. There is currently no cure for Jung syndrome, and management focuses on improving quality of life and addressing specific medical needs as they arise.

Key symptoms:

Narrow eye openings (blepharophimosis)Drooping eyelids (ptosis)Webbing or fusion of fingers or toes (syndactyly)Short statureBroad nasal bridgeFlat midfaceSmall jawLow-set earsSkeletal abnormalitiesPossible mild intellectual disability

Clinical phenotype terms (17)— hover any for plain English
Tracheal stenosisHP:0002777
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Jung syndrome.

View clinical trials →

No actively recruiting trials found for Jung syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Jung syndrome community →

No specialists are currently listed for Jung syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Jung syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Jung syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features of Jung syndrome does my child have, and how severe are they?,Is surgery recommended for the eyelid drooping or finger/toe webbing, and when is the best time?,Should we pursue genetic testing to try to identify the exact genetic cause?,What specialists should we see regularly, and how often?,Are there any vision concerns we should watch for?,Will my child's growth be significantly affected, and should we see an endocrinologist?,What is the chance of having another child with this condition?

Common questions about Jung syndrome

What is Jung syndrome?

Jung syndrome, also known as Jung-Bhatt-Bhatt syndrome or blepharophimosis with ptosis, syndactyly, and short stature, is an extremely rare genetic condition that affects multiple parts of the body. It was first described in the medical literature and is characterized by a combination of eye, hand, and growth abnormalities. People with Jung syndrome typically have narrow eye openings (blepharophimosis) and drooping eyelids (ptosis), which can affect vision and facial appearance. They may also have webbing or fusion of fingers or toes (syndactyly) and shorter-than-expected height (short stature

How is Jung syndrome inherited?

Jung syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Jung syndrome typically begin?

Typical onset of Jung syndrome is neonatal. Age of onset can vary across affected individuals.