Intellectual disability-facial dysmorphism-hand anomalies syndrome

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Overview

Intellectual disability-facial dysmorphism-hand anomalies syndrome is an extremely rare genetic condition that affects brain development, facial features, and the structure of the hands. Children born with this syndrome typically show intellectual disability ranging from mild to severe, meaning they may have difficulty learning, reasoning, and developing skills at the same pace as other children their age. The facial features associated with this condition can include an unusually shaped face, widely spaced eyes, a broad or flat nasal bridge, and other subtle differences in facial structure that a trained geneticist may recognize. Hand anomalies can include short fingers (brachydactyly), curved fingers (clinodactyly), or other structural differences in the hands that may affect fine motor skills. Because this syndrome is so rare, the treatment landscape is largely supportive rather than curative. Management focuses on early intervention programs, special education services, speech and occupational therapy, and addressing any specific medical complications as they arise. Regular follow-up with a team of specialists is important to monitor development and provide the best possible support for affected individuals and their families.

Key symptoms:

Intellectual disabilityDelayed speech and language developmentUnusual facial featuresShort fingersCurved fingersWidely spaced eyesBroad or flat nasal bridgeLow-set earsDelayed motor milestonesLearning difficultiesHand abnormalitiesShort statureBehavioral challenges

Clinical phenotype terms (34)— hover any for plain English
Broad chinHP:0011822Short palpebral fissureHP:0012745Facial grimacingHP:0000273Abnormal scalp morphologyHP:0001965Cervical C2/C3 vertebral fusionHP:0004602
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Intellectual disability-facial dysmorphism-hand anomalies syndrome.

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No actively recruiting trials found for Intellectual disability-facial dysmorphism-hand anomalies syndrome at this time.

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No specialists are currently listed for Intellectual disability-facial dysmorphism-hand anomalies syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Intellectual disability-facial dysmorphism-hand anomalies syndrome.

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Community

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Caregiver Resources

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Family & Caregiver Grants

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the specific genetic cause of my child's condition, and should other family members be tested?,What therapies and early intervention services do you recommend starting right away?,How severe is the intellectual disability, and what level of independence can we expect over time?,Are there any surgical options to improve hand function?,What educational supports should we request from our school district?,Are there any clinical trials or research studies we should know about?,How often should we schedule follow-up appointments, and with which specialists?

Common questions about Intellectual disability-facial dysmorphism-hand anomalies syndrome

What is Intellectual disability-facial dysmorphism-hand anomalies syndrome?

Intellectual disability-facial dysmorphism-hand anomalies syndrome is an extremely rare genetic condition that affects brain development, facial features, and the structure of the hands. Children born with this syndrome typically show intellectual disability ranging from mild to severe, meaning they may have difficulty learning, reasoning, and developing skills at the same pace as other children their age. The facial features associated with this condition can include an unusually shaped face, widely spaced eyes, a broad or flat nasal bridge, and other subtle differences in facial structure th

How is Intellectual disability-facial dysmorphism-hand anomalies syndrome inherited?

Intellectual disability-facial dysmorphism-hand anomalies syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Intellectual disability-facial dysmorphism-hand anomalies syndrome typically begin?

Typical onset of Intellectual disability-facial dysmorphism-hand anomalies syndrome is neonatal. Age of onset can vary across affected individuals.