Idiopathic spontaneous coronary artery dissection

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ORPHA:458718OMIM:122455I25.4
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2Active trials8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Idiopathic spontaneous coronary artery dissection (sometimes called idiopathic SCAD) is a rare and potentially life-threatening heart condition in which the wall of a coronary artery — one of the blood vessels that supplies the heart muscle — tears open without any obvious cause. When this tear occurs, blood can become trapped between the layers of the artery wall, forming a blockage that reduces or stops blood flow to part of the heart. This can lead to a heart attack, even in people who are otherwise young and healthy with no traditional risk factors like high cholesterol or smoking. The term 'idiopathic' means that no clear underlying cause — such as a known connective tissue disorder, fibromuscular dysplasia, or trauma — has been identified. The most common symptom is sudden, severe chest pain, which may feel like pressure, squeezing, or burning. Other symptoms can include shortness of breath, nausea, sweating, dizziness, and pain radiating to the arm, jaw, or back. Some patients experience cardiac arrest. SCAD disproportionately affects women, particularly those in their 40s and 50s, and has been associated with emotional or physical stress, pregnancy, and hormonal factors. Treatment depends on the severity and may range from conservative medical management with blood thinners and heart medications to procedures like stenting or bypass surgery in more serious cases. Because SCAD can recur, long-term follow-up with a cardiologist is essential. Research into the causes and best treatments for idiopathic SCAD is still ongoing.

Also known as:

Key symptoms:

Sudden severe chest painChest pressure or tightnessPain spreading to the arm, jaw, neck, or backShortness of breathNausea or vomitingExcessive sweatingDizziness or lightheadednessFeeling of extreme fatigueRapid or irregular heartbeatFainting or loss of consciousnessHeart attack symptoms in a young, otherwise healthy person

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗OMIM ↗NORD ↗

FDA & Trial Timeline

3 events
Feb 2025Impact of CYP2C19 Genotype-guided Approach in Antiplatelet Therapy on Platelet Reactivity Index Among Coronary Artery Disease (CAD) Patients

Nur Hafizah Annezah binti Utuh — PHASE4

TrialNOT YET RECRUITING
Mar 2019International Spontaneous Coronary Artery Dissection (SCAD) "iSCAD" Registry

SCAD Alliance

TrialRECRUITING
Jan 2015Clinical Cohort Study - INTERCATH

University of Hamburg-Eppendorf

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Idiopathic spontaneous coronary artery dissection.

2 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

2 recruitingView all trials with filters →
Other2 trials
International Spontaneous Coronary Artery Dissection (SCAD) "iSCAD" Registry
Actively Recruiting
PI: Esther Kim, MD (Chair, Steering Committee) · Sites: Los Angeles, California; Los Angeles, California +29 more · Age: 1899 yrs
Clinical Cohort Study - INTERCATH
Active
· Sites: Hamburg · Age: 1899 yrs

No specialists are currently listed for Idiopathic spontaneous coronary artery dissection.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Idiopathic spontaneous coronary artery dissection.

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Community

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Caregiver Resources

NORD Caregiver Resources

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What caused my SCAD, and is there anything that can be done to prevent it from happening again?,Should I be screened for fibromuscular dysplasia or connective tissue disorders?,What medications do I need to take long-term, and what are their side effects?,What level of physical activity is safe for me now, and will that change over time?,Is it safe for me to become pregnant in the future?,Should my family members be screened or tested for anything?,How often do I need follow-up imaging or cardiology appointments?

Common questions about Idiopathic spontaneous coronary artery dissection

What is Idiopathic spontaneous coronary artery dissection?

Idiopathic spontaneous coronary artery dissection (sometimes called idiopathic SCAD) is a rare and potentially life-threatening heart condition in which the wall of a coronary artery — one of the blood vessels that supplies the heart muscle — tears open without any obvious cause. When this tear occurs, blood can become trapped between the layers of the artery wall, forming a blockage that reduces or stops blood flow to part of the heart. This can lead to a heart attack, even in people who are otherwise young and healthy with no traditional risk factors like high cholesterol or smoking. The te

How is Idiopathic spontaneous coronary artery dissection inherited?

Idiopathic spontaneous coronary artery dissection follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Idiopathic spontaneous coronary artery dissection typically begin?

Typical onset of Idiopathic spontaneous coronary artery dissection is adult. Age of onset can vary across affected individuals.

Are there clinical trials for Idiopathic spontaneous coronary artery dissection?

Yes — 2 recruiting clinical trials are currently listed for Idiopathic spontaneous coronary artery dissection on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.