Idiopathic giant cell myocarditis

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2Specialists8Treatment centers

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Overview

Idiopathic giant cell myocarditis (GCM) is a rare and serious inflammatory disease of the heart muscle. The word "idiopathic" means the exact cause is unknown. In this condition, the immune system attacks the heart muscle, and large cells called "giant cells" (formed by fused immune cells) are found in the heart tissue. This leads to severe inflammation and damage to the heart. The disease mainly affects young to middle-aged adults and can progress rapidly. Common symptoms include heart failure (shortness of breath, swelling in the legs, fatigue), abnormal heart rhythms (palpitations, fainting, or sudden cardiac arrest), and chest pain. Some patients may also develop blood clots. Because the heart's pumping ability can decline quickly, this condition can become life-threatening within weeks to months if not treated. Treatment typically involves strong medications that suppress the immune system, such as cyclosporine, corticosteroids, and other immunosuppressive drugs. Many patients eventually require a heart transplant. While treatment can slow the disease and improve symptoms, giant cell myocarditis remains one of the most aggressive forms of myocarditis. Early diagnosis through heart biopsy is critical because it allows doctors to start the right treatment as soon as possible. About 20-25% of patients with GCM also have another autoimmune condition, such as inflammatory bowel disease or thyroid disease.

Also known as:

Key symptoms:

Shortness of breath, especially with activity or lying downRapid or irregular heartbeat (palpitations)Chest painSevere fatigue and weaknessSwelling in the legs, ankles, or feetFainting or near-fainting episodesSudden cardiac arrestDizziness or lightheadednessInability to exercise or do normal activitiesFluid buildup in the lungsUnexplained weight gain from fluid retentionLow blood pressure

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Idiopathic giant cell myocarditis.

View clinical trials →

No actively recruiting trials found for Idiopathic giant cell myocarditis at this time.

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Specialists

2 foundView all specialists →
LM
Leslie T Cooper, MD
Specialist
PI on 1 active trial1 Idiopathic giant cell myocarditis publication
OJ
Oscar M P Jolobe
Specialist
1 Idiopathic giant cell myocarditis publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Idiopathic giant cell myocarditis.

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Community

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Latest news about Idiopathic giant cell myocarditis

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is the damage to my heart, and what is my current heart function?,What immunosuppressive medications do you recommend, and what are the main side effects?,Am I likely to need a heart transplant, and when should we start planning for that?,Should I have an implantable defibrillator (ICD) to protect against dangerous heart rhythms?,What activity restrictions should I follow, and when might I be able to return to normal activities?,How often will I need follow-up visits, biopsies, or imaging tests?,Are there any clinical trials or new treatments I should consider?

Common questions about Idiopathic giant cell myocarditis

What is Idiopathic giant cell myocarditis?

Idiopathic giant cell myocarditis (GCM) is a rare and serious inflammatory disease of the heart muscle. The word "idiopathic" means the exact cause is unknown. In this condition, the immune system attacks the heart muscle, and large cells called "giant cells" (formed by fused immune cells) are found in the heart tissue. This leads to severe inflammation and damage to the heart. The disease mainly affects young to middle-aged adults and can progress rapidly. Common symptoms include heart failure (shortness of breath, swelling in the legs, fatigue), abnormal heart rhythms (palpitations, faintin

How is Idiopathic giant cell myocarditis inherited?

Idiopathic giant cell myocarditis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Idiopathic giant cell myocarditis typically begin?

Typical onset of Idiopathic giant cell myocarditis is adult. Age of onset can vary across affected individuals.

Which specialists treat Idiopathic giant cell myocarditis?

2 specialists and care centers treating Idiopathic giant cell myocarditis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.