Histoplasmosis

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1Active trials20Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Histoplasmosis is an infection caused by a fungus called Histoplasma capsulatum. It is sometimes called 'cave disease' or 'Ohio Valley disease' because the fungus is very common in certain parts of the world, especially in river valleys. People get infected by breathing in tiny fungal spores from the environment, often from soil that contains bird or bat droppings. Most healthy people who breathe in these spores never feel sick at all, or they may have only mild flu-like symptoms that go away on their own. However, in some people — especially those with weakened immune systems, very young children, or older adults — the infection can become serious and spread throughout the body. When histoplasmosis does cause symptoms, it most often affects the lungs. People may experience fever, cough, fatigue, and chest pain. In more severe cases, the infection can spread to other organs like the liver, spleen, bone marrow, and brain. This severe form is called disseminated histoplasmosis and can be life-threatening if not treated quickly. The good news is that histoplasmosis can be treated with antifungal medicines. Mild cases may not need any treatment at all. Moderate to severe cases are treated with antifungal drugs such as itraconazole or amphotericin B, which are well-established and effective. With proper treatment, most people recover fully. Long-term treatment may be needed for people with weakened immune systems to prevent the infection from coming back.

Also known as:

Key symptoms:

FeverCoughFatigue and tirednessChest pain or tightnessShortness of breathHeadacheMuscle aches and joint painChills and sweatingUnintended weight lossEnlarged lymph nodesEnlarged liver or spleenMouth sores or skin lesions (in severe cases)Confusion or neurological symptoms (in severe cases)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
May 2026Histoplasmosis Induction and Consolidation Therapy Factorial Randomized Clinical Trial (Histo-FACT)

University of Minnesota — PHASE3

TrialNOT YET RECRUITING
Jan 2025Efficacy and Safety of High-dose Liposomal Amphotericin B for Disseminated Histoplasmosis in AIDS

Federal University of Health Science of Porto Alegre — PHASE3

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Histoplasmosis.

1 clinical trialare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

1 recruitingView all trials with filters →
Phase 31 trial
Efficacy and Safety of High-dose Liposomal Amphotericin B for Disseminated Histoplasmosis in AIDS
Phase 3
Actively Recruiting
PI: Daiane F Dalla Lana, PhD (Federal University of Health Science of Porto Aleg) · Sites: Goiânia, Goiás; Natal, Rio Grande do Norte +3 more · Age: 1899 yrs

Specialists

20 foundView all specialists →
KM
Kevin J Blinder, MD
BRENTWOOD, MO
Specialist
PI on 1 active trial
BM
Brad Sawtelle, M.D.
LINCOLN, NE
Specialist
PI on 1 active trial
RM
Royce Johnson, M.D.
BAKERSFIELD, CA
Specialist
PI on 1 active trial
NM
Neil Ampel, M.D.
SCOTTSDALE, AZ
Specialist
PI on 1 active trial
HP
Harry S Nielsen, Ph.D.
Specialist
PI on 2 active trials
SD
Stephen Kernerman, D.O.
SPOKANE, WA
Specialist
PI on 1 active trial
KP
Kyun-Seop Bae, M.D., Ph.D.
Specialist
PI on 1 active trial
HM
Hamid Ahmadieh, MD
Specialist
PI on 8 active trials
AM
Ahmad M Mansour, MD
Specialist
PI on 3 active trials
AM
Andrej Spec, MD
SAINT LOUIS, MO
Specialist
PI on 2 active trials1 Histoplasmosis publication
PM
Peter G Pappas, MD
Specialist
PI on 1 active trial
LW
LJ Wheat
Specialist
PI on 1 active trial
JK
John W Kitchens
LEXINGTON, KY
Specialist
PI on 1 active trial
NB
Nathan Bahr
MINNEAPOLIS, MN
Specialist
PI on 1 active trial
WL
Wheat LJ
Specialist
PI on 1 active trial
MG
Mitch Goldman
Specialist
PI on 1 active trial
DL
Daiane Dalla Lana
Specialist
PI on 1 active trial
DL
Daiane F Dalla Lana
Specialist
PI on 1 active trial
JK
John Kitchens
LEXINGTON, KY
Specialist
PI on 1 active trial
GS
Gaurav K Shah
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Histoplasmosis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Histoplasmosis

Disease timeline:

New recruiting trial: Efficacy and Safety of High-dose Liposomal Amphotericin B for Disseminated Histoplasmosis in AIDS

A new clinical trial is recruiting patients for Histoplasmosis

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Do I need antifungal treatment, or can my body fight this infection on its own?,How long will I need to take antifungal medication, and what side effects should I watch for?,Are there any activities or environments I should avoid while I am infected or recovering?,How will we know if the treatment is working, and what tests will be used to monitor my progress?,Is there a risk that the infection could come back, and if so, how can we prevent that?,Should other members of my household or people I was with be tested or evaluated?,Do I need to see any other specialists, such as a lung doctor or an immune system specialist?

Common questions about Histoplasmosis

What is Histoplasmosis?

Histoplasmosis is an infection caused by a fungus called Histoplasma capsulatum. It is sometimes called 'cave disease' or 'Ohio Valley disease' because the fungus is very common in certain parts of the world, especially in river valleys. People get infected by breathing in tiny fungal spores from the environment, often from soil that contains bird or bat droppings. Most healthy people who breathe in these spores never feel sick at all, or they may have only mild flu-like symptoms that go away on their own. However, in some people — especially those with weakened immune systems, very young chil

How is Histoplasmosis inherited?

Histoplasmosis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Are there clinical trials for Histoplasmosis?

Yes — 1 recruiting clinical trial is currently listed for Histoplasmosis on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Histoplasmosis?

20 specialists and care centers treating Histoplasmosis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.