Hallermann-Streiff-like syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:2109Q87.0
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Hallermann-Streiff-like syndrome is an extremely rare genetic condition that shares many features with classic Hallermann-Streiff syndrome but may have distinct underlying causes or slightly different presentations. The condition primarily affects the face, eyes, skin, hair, and bones. People with this syndrome typically have a characteristic facial appearance that may include a small jaw (micrognathia), a beaked or thin nose, and a small mouth. Eye problems are common and can include cataracts present at birth, small eyes (microphthalmia), and other vision difficulties. The skull may have an unusual shape, and the skin can appear thin or aged-looking, with sparse hair on the scalp, eyebrows, and eyelashes. Dental abnormalities such as extra teeth at birth (natal teeth), missing teeth, or malformed teeth are also frequently seen. Short stature and proportionate dwarfism may occur. Some individuals may have mild to moderate intellectual disability, though many have normal intelligence. There is currently no cure for this condition, and treatment focuses on managing individual symptoms. This may include eye surgery for cataracts, dental care, nutritional support if feeding difficulties are present, and monitoring of growth and development. A team of specialists is usually needed to provide comprehensive care throughout life.

Also known as:

Key symptoms:

Small jaw and receding chinThin or beaked noseCataracts present at birthSmall eyesThin or aged-looking skinSparse hair on the scalp, eyebrows, and eyelashesShort statureDental abnormalities including teeth present at birthUnusual skull shapeSmall mouthFeeding difficulties in infancyBreathing difficulties due to small airwayVision problemsPossible mild intellectual disabilityFragile bones

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Hallermann-Streiff-like syndrome.

View clinical trials →

No actively recruiting trials found for Hallermann-Streiff-like syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Hallermann-Streiff-like syndrome community →

No specialists are currently listed for Hallermann-Streiff-like syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Hallermann-Streiff-like syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Hallermann-Streiff-like syndromeForum →

No community posts yet. Be the first to share your experience with Hallermann-Streiff-like syndrome.

Start the conversation →

Latest news about Hallermann-Streiff-like syndrome

No recent news articles for Hallermann-Streiff-like syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features does my child have that led to this diagnosis, and how is it different from classic Hallermann-Streiff syndrome?,Should we pursue genetic testing, and what type of testing do you recommend?,When should cataract surgery be performed, and what are the expected outcomes?,Are there any airway concerns we should be monitoring at home?,What specialists should be part of our care team, and how often should we see them?,Are there any clinical trials or research studies we could participate in?,What developmental milestones should we watch for, and when should we seek early intervention?

Common questions about Hallermann-Streiff-like syndrome

What is Hallermann-Streiff-like syndrome?

Hallermann-Streiff-like syndrome is an extremely rare genetic condition that shares many features with classic Hallermann-Streiff syndrome but may have distinct underlying causes or slightly different presentations. The condition primarily affects the face, eyes, skin, hair, and bones. People with this syndrome typically have a characteristic facial appearance that may include a small jaw (micrognathia), a beaked or thin nose, and a small mouth. Eye problems are common and can include cataracts present at birth, small eyes (microphthalmia), and other vision difficulties. The skull may have an

At what age does Hallermann-Streiff-like syndrome typically begin?

Typical onset of Hallermann-Streiff-like syndrome is neonatal. Age of onset can vary across affected individuals.