Growth delay-intellectual disability-hepatopathy syndrome

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ORPHA:541423OMIM:617093K76.8
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8Treatment centers

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Overview

Growth delay-intellectual disability-hepatopathy syndrome is a rare genetic condition that affects multiple parts of the body, most notably causing slow growth, learning and developmental challenges, and liver problems. The syndrome is sometimes referred to by its shorthand initials or described as a combined metabolic and developmental disorder. Children with this condition often grow more slowly than their peers, reach developmental milestones later than expected, and may have varying degrees of intellectual disability ranging from mild to more significant. The liver (hepatopathy) involvement can range from mildly abnormal liver enzyme levels to more serious liver dysfunction, which requires careful monitoring over time. Because this syndrome affects several body systems at once, children typically need care from a team of specialists including geneticists, liver specialists, and developmental pediatricians. There is currently no cure for this condition, and treatment focuses on managing symptoms, supporting development through therapies, and monitoring liver health. Early diagnosis and a coordinated care plan can make a meaningful difference in quality of life and long-term outcomes for affected children and their families.

Key symptoms:

Slower than normal growth and short statureIntellectual disability or learning difficultiesDelayed developmental milestones such as sitting, walking, and talkingLiver disease or abnormal liver functionLow muscle tone (floppiness in infancy)Feeding difficulties in infancyAbnormal liver enzyme levels on blood testsEnlarged liver (hepatomegaly) in some casesSpeech and language delaysBehavioral challenges

Clinical phenotype terms (35)— hover any for plain English
Decreased serum zincHP:0031831Duplicated collecting systemHP:0000081
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Growth delay-intellectual disability-hepatopathy syndrome.

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No actively recruiting trials found for Growth delay-intellectual disability-hepatopathy syndrome at this time.

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No specialists are currently listed for Growth delay-intellectual disability-hepatopathy syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Growth delay-intellectual disability-hepatopathy syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific changes were found in the NBAS gene, and what do they mean for my child's health?,How often should my child's liver function be tested, and what signs should prompt an urgent visit?,What should I do if my child gets a fever or becomes very ill — is there an emergency protocol I should follow?,What therapies (speech, occupational, physical) does my child need, and how do I access them?,Are there any dietary changes or restrictions that will help protect my child's liver?,What is the risk of this condition occurring in future pregnancies, and should other family members be tested?,Are there any clinical trials or research studies my child might be eligible to participate in?

Common questions about Growth delay-intellectual disability-hepatopathy syndrome

What is Growth delay-intellectual disability-hepatopathy syndrome?

Growth delay-intellectual disability-hepatopathy syndrome is a rare genetic condition that affects multiple parts of the body, most notably causing slow growth, learning and developmental challenges, and liver problems. The syndrome is sometimes referred to by its shorthand initials or described as a combined metabolic and developmental disorder. Children with this condition often grow more slowly than their peers, reach developmental milestones later than expected, and may have varying degrees of intellectual disability ranging from mild to more significant. The liver (hepatopathy) involvemen

How is Growth delay-intellectual disability-hepatopathy syndrome inherited?

Growth delay-intellectual disability-hepatopathy syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Growth delay-intellectual disability-hepatopathy syndrome typically begin?

Typical onset of Growth delay-intellectual disability-hepatopathy syndrome is infantile. Age of onset can vary across affected individuals.