Frontotemporal neurodegeneration with movement disorder

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ORPHA:306708
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Overview

Frontotemporal neurodegeneration with movement disorder is a rare genetic brain disease that affects the front and side parts of the brain (the frontal and temporal lobes). These brain regions control personality, behavior, language, and movement. Over time, nerve cells in these areas break down and die, leading to a combination of thinking and behavior changes along with movement problems. Patients may notice changes in personality, difficulty with language or speech, and problems with coordination or involuntary movements such as tremors, stiffness, or difficulty walking. The disease typically begins in adulthood and gets worse over time. Because it affects both thinking and movement, it can be confused with other conditions like Parkinson's disease or other forms of frontotemporal dementia. There is currently no cure for this condition. Treatment focuses on managing symptoms, such as medications for movement difficulties, speech therapy, and behavioral support. Research is ongoing to better understand the genetic causes and to develop treatments that may slow or stop the disease from progressing.

Key symptoms:

Changes in personality or behaviorDifficulty with speech or finding wordsProblems with planning and decision-makingTremors or shakingMuscle stiffness or rigiditySlow movementsDifficulty walking or balance problemsMemory loss that worsens over timeLoss of empathy or social awarenessInvoluntary muscle movementsDifficulty swallowingApathy or lack of motivationRepetitive or compulsive behaviorsPoor coordination

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Frontotemporal neurodegeneration with movement disorder.

View clinical trials →

No actively recruiting trials found for Frontotemporal neurodegeneration with movement disorder at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Frontotemporal neurodegeneration with movement disorder community →

No specialists are currently listed for Frontotemporal neurodegeneration with movement disorder.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Frontotemporal neurodegeneration with movement disorder.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Frontotemporal neurodegeneration with movement disorder

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic mutation is causing this condition in my case?,How quickly is this disease likely to progress for me?,Are there any clinical trials I might be eligible for?,What medications or therapies can help manage my symptoms right now?,Should my family members be tested for the genetic mutation?,What support services are available for me and my caregivers?,When should we start planning for advanced care needs?

Common questions about Frontotemporal neurodegeneration with movement disorder

What is Frontotemporal neurodegeneration with movement disorder?

Frontotemporal neurodegeneration with movement disorder is a rare genetic brain disease that affects the front and side parts of the brain (the frontal and temporal lobes). These brain regions control personality, behavior, language, and movement. Over time, nerve cells in these areas break down and die, leading to a combination of thinking and behavior changes along with movement problems. Patients may notice changes in personality, difficulty with language or speech, and problems with coordination or involuntary movements such as tremors, stiffness, or difficulty walking. The disease typical

At what age does Frontotemporal neurodegeneration with movement disorder typically begin?

Typical onset of Frontotemporal neurodegeneration with movement disorder is adult. Age of onset can vary across affected individuals.