Fetal encasement syndrome

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ORPHA:465824OMIM:613630Q87.8
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Overview

Fetal encasement syndrome is an extremely rare condition that is present at birth. In this syndrome, the baby is born with skin that is abnormally tight, thick, or rigid, giving the appearance that the body is encased or wrapped in a restrictive layer. This condition can severely limit the movement of the limbs and joints, and it may also affect the face and other parts of the body. The tight skin can restrict normal growth and development of the underlying tissues, including muscles and bones. Babies born with this condition often have joint contractures, meaning their joints are fixed in a bent or straight position and cannot move freely. Facial features may also be affected, with a mask-like appearance due to the tightness of the skin over the face. Breathing difficulties can occur if the chest wall is restricted. Because this condition is so rare, there is very limited information about its causes and treatment options. Management is primarily supportive and focuses on addressing the specific symptoms each child experiences. A team of specialists is usually needed to provide the best possible care. The long-term outlook depends on the severity of the condition and which body systems are affected.

Key symptoms:

Extremely tight or rigid skin at birthLimited movement of arms and legsJoint contractures (joints stuck in one position)Mask-like facial appearanceDifficulty breathingRestricted chest wall movementDifficulty feedingSwelling of the skinAbnormal skin texture or appearanceRestricted growthLimited facial expressionsDifficulty opening the mouth fully

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Fetal encasement syndrome.

View clinical trials →

No actively recruiting trials found for Fetal encasement syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Fetal encasement syndrome community →

No specialists are currently listed for Fetal encasement syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Fetal encasement syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Fetal encasement syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my child's condition, and which parts of the body are most affected?,What is the expected outlook for my child based on their specific symptoms?,What therapies and treatments should we start right away?,Are there any genetic tests that could help us understand the cause?,What emergency signs should we watch for at home?,Are there any other families or support groups dealing with this condition?,Should we consider genetic counseling for future pregnancies?

Common questions about Fetal encasement syndrome

What is Fetal encasement syndrome?

Fetal encasement syndrome is an extremely rare condition that is present at birth. In this syndrome, the baby is born with skin that is abnormally tight, thick, or rigid, giving the appearance that the body is encased or wrapped in a restrictive layer. This condition can severely limit the movement of the limbs and joints, and it may also affect the face and other parts of the body. The tight skin can restrict normal growth and development of the underlying tissues, including muscles and bones. Babies born with this condition often have joint contractures, meaning their joints are fixed in a b

How is Fetal encasement syndrome inherited?

Fetal encasement syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Fetal encasement syndrome typically begin?

Typical onset of Fetal encasement syndrome is neonatal. Age of onset can vary across affected individuals.